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El. knyga: CURRENT Diagnosis and Treatment Pediatrics, Twenty-Fifth Edition

4.16/5 (75 ratings by Goodreads)
  • Formatas: 1504 pages
  • Išleidimo metai: 06-May-2020
  • Leidėjas: McGraw-Hill Education
  • Kalba: eng
  • ISBN-13: 9781260457810
Kitos knygos pagal šią temą:
  • Formatas: 1504 pages
  • Išleidimo metai: 06-May-2020
  • Leidėjas: McGraw-Hill Education
  • Kalba: eng
  • ISBN-13: 9781260457810
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The most practical, up-to-date, and well-referenced guide to the diagnosis and treatment of children—from birth to adolescence

Following the "Current" outline format to make it super easy for you to find the answers you need, this comprehensive, clinically focused guide delivers evidence-based information on the pediatric medical conditions most often encountered in daily clinical practice.

Complete with an invaluable guide to normal laboratory values and 600 photos and illustrations, CURRENT Diagnosis and Treatment Pediatrics offers succinct, authoritative overviews of important pediatric health concerns, such as childhood nutrition and eating disorders; substance abuse; psychiatric disorders; child abuse; oral medicine and dentistry; immunization; and emergencies and injuries. The authors provide detailed descriptions of diseases as well as diagnostic and therapeutic procedures, and everything is presented in the time-saving LANGE CURRENT style: Problem, Essentials of Diagnosis, Clinical Findings, Differential Diagnosis, Treatment, and Prognosis.



Authors xix
Preface xxix
Milestone 25th Silver Anniversary Edition xxxi
1 Advancing the Quality & Safety of Care
1(9)
Daniel Hyman
Introduction
1(1)
Current Context
1(3)
Strategies & Models for Quality Improvement (QI)
4(3)
Principles of Patient Safety (Incident Reporting, Just Culture, Disclosure, FMEA, RCA, Reliability, Data, & Checklists)
7(3)
2 The Newborn Infant
10(56)
Danielle Smith
Introduction
10(1)
The Neonatal History
10(1)
Assessment of Growth & Gestational Age
10(2)
Examination at Birth
12(1)
Examination in the Nursery
12(3)
Care of the Well Neonate
15(3)
Feeding the Well Neonate
15(1)
Early Discharge of the Newborn Infant
16(1)
Hearing Screening
17(1)
Common Problems in the Term Newborn
18(13)
Neonatal Jaundice
18(6)
Hypoglycemia
24(2)
Respiratory Distress in the Term Newborn Infant
26(2)
Heart Murmurs
28(1)
Birth Trauma
28(1)
Infants of Mothers Who Abuse Drugs
29(2)
Multiple Births
31(1)
Neonatal Intensive Care
31(14)
Perinatal Resuscitation
31(4)
The Preterm Infant
35(9)
The Late Preterm Infant
44(1)
Cardiac Problems in the Newborn Infant
45(2)
Structural Heart Disease
45(1)
Persistent Pulmonary Hypertension
46(1)
Arrhythmias
47(1)
Gastrointestinal & Abdominal Surgical Conditions in the Newborn Infant
47(4)
Esophageal Atresia & Tracheoesophageal Fistula
47(1)
Intestinal Obstruction
48(1)
Abdominal Wall Defects
49(1)
Diaphragmatic Hernia
50(1)
Gastrointestinal Bleeding
50(1)
Gastroesophageal Reflux
51(1)
Infections in the Newborn Infant
51(7)
Bacterial Infections
51(3)
Fungal Sepsis
54(1)
Congenital Infections
55(2)
Perinatally Acquired Infections
57(1)
Hematologic Disorders in the Newborn Infant
58(3)
Bleeding Disorders
58(2)
Anemia
60(1)
Polycythemia
60(1)
Renal Disorders in the Newborn Infant
61(1)
Renal Failure
61(1)
Urinary Tract Anomalies
61(1)
Renal Vein Thrombosis
62(1)
Neurologic Problems in the Newborn Infant
62(2)
Seizures
62(1)
Intracranial Hemorrhage
63(1)
Metabolic Disorders in the Newborn Infant
64(1)
Hyperglycemia
64(1)
Hypocalcemia
64(1)
Inborn Errors of Metabolism
65(1)
Quality Assessment & Improvement in the Newborn Nursery & NICU
65(1)
3 Child Development & Behavior
66(31)
Edward Goldson
Ann Reynolds
Abigail S. Angulo
Dannah M. Raz
Introduction
66(1)
Normal Development
66(7)
The First 2 Years
66(6)
Ages 2-4 Years
72(1)
Early School Years: Ages 5-7 Years
72(1)
Middle Childhood: Ages 7-11 Years
73(1)
Behavioral & Developmental Variations
73(1)
Normality & Temperament
73(1)
Enuresis & Encopresis
74(2)
Enuresis
74(1)
Encopresis
75(1)
Common Developmental Concerns
76(1)
Colic
76(1)
Feeding Disorders in Infants & Young Children
77(7)
Sleep Disorders
79(1)
Parasomnias
80(1)
Insomnia
80(1)
Sleep-Disordered Breathing
81(1)
Restless Legs Syndrome & Periodic Limb Movement Disorder
81(1)
Temper Tantrums & Breath-Holding Spells
82(2)
Well-Child Surveillance & Screening
84(13)
Developmental Disorders
84(1)
Attention-Deficit/Hyperactivity Disorder
85(3)
Autism Spectrum Disorders
88(4)
Intellectual Disability
92(2)
Specific Forms of Intellectual Disability & Associated Treatment Issues
94(2)
References
96(1)
4 Adolescence
97(43)
Amy E. Sass
Molly J. Richards
Introduction
97(1)
Epidemiology
97(1)
Mortality Data
97(1)
Morbidity Data
97(1)
Providing A Medical Home for Adolescents
98(1)
Relating to the Adolescent Patient
99(7)
The Structure of the Visit
100(6)
Guidelines for Adolescent Preventive Services
106(6)
Adolescent Screening
106(4)
Promoting Healthy Behaviors
110(2)
Transition to Adult Care
112(1)
Growth & Development
112(4)
Puberty
112(1)
Physical Growth
113(1)
Sexual Maturation
113(1)
Psychosocial Development
114(2)
Adolescent Gynecology & Reproductive Health
116(24)
Breast Examination
116(1)
Breast Masses
116(2)
Nipple Discharge & Galactorrhea
118(1)
Gynecomastia
119(1)
Gynecologic Care & Gynecologic Disorders in Adolescence
120(11)
Contraception
131(6)
Pregnancy
137(3)
5 Adolescent Substance Abuse
140(15)
Paritosh Kaul
Scope of the Problem
140(5)
Morbidity Data
145(1)
Predicting the Progression From Use to Abuse
146(1)
Evaluation of Substance Abuse
146(4)
Treatment & Referral
150(3)
Prevention
153(1)
References
154(1)
6 Eating Disorders
155(12)
Eric J. Sigel
Introduction
155(1)
Etiology
155(1)
Incidence
156(1)
Predisposing Factors & Clinical Profiles
156(1)
Anorexia Nervosa
156(6)
Bulimia Nervosa
162(2)
Binge-Eating Disorder
164(1)
Avoidant/Restrictive Food Intake Disorder
165(1)
Prognosis, Quality Assessment, & Outcomes Metrics
165(1)
Resources for Practitioners & Families
166(1)
7 Child & Adolescent Psychiatric Disorders & Psychosocial Aspects of Pediatrics
167(41)
Kimberly Kelsay
AyeletTalmi
Adam Burstein
Introduction
167(10)
Models of Care Encompassing Behavioral Health in the Primary Care Setting
168(1)
Prevention, Early Identification, & Developmental Context
168(2)
Lifestyle Recommendations
170(1)
Identification & Assessment During Health Supervision Visits
170(1)
Tools for Mental Health Screening in the Primary Care Office Setting
171(6)
Psychiatric Disorders of Childhood & Adolescence
177(7)
Anxiety Disorders
178(6)
Obsessive-Compulsive & Related Disorders
184(24)
Attention-Deficit/Hyperactivity Disorder
187(2)
Mood Disorders
189(6)
Suicide in Children & Adolescents
195(1)
Disruptive, Impulse-Control, & Conduct Disorders
196(2)
High-Risk Patients & Homicide
198(1)
Somatic Symptom & Related Disorders
199(2)
Adjustment Disorders
201(1)
Psychotic Disorders
201(2)
Other Psychiatric Conditions
203(1)
References
204(4)
8 Child Abuse & Neglect
208(9)
Antonia Chiesa
Andrew P. Sirotnak
Introduction
208(1)
Prevention
209(1)
Clinical Findings
210(5)
Differential Diagnosis
215(1)
Treatment
215(1)
Prognosis
216(1)
9 Ambulatory & Office Pediatrics
217(23)
Meghan Treitz
Daniel Nicklas
David Fox
Introduction
217(1)
Pediatric History
217(1)
Pediatric Physical Examination
218(1)
Health Supervision Visits
219(14)
Developmental & Behavioral Assessment
219(3)
Growth Parameters
222(1)
Blood Pressure
223(1)
Vision & Hearing Screening
224(4)
Anticipatory Guidance
228(2)
Nutrition Counseling
230(1)
Counseling About Television & Other Media
230(1)
Immunizations
231(1)
Acute-Care Visits
232(1)
Prenatal Visits
232(1)
Sports Physicals
232(1)
Chronic Disease Management
233(1)
Medical Home
233(1)
Mental & Behavioral Health
233(1)
Telephone Management & Web-Based Information
234(1)
Advocacy & Community Pediatrics
235(1)
Toxic Stress
235(1)
Common General Pediatric Issues
236(4)
Fever
236(1)
Growth Deficiency
237(3)
10 Immunization
240(36)
Matthew F. Daley
Sean T. O'leary
Ann-Christine Nyquist
Jessica R. Cataldi
Standards for Pediatric Immunization Practices
241(1)
Routine Childhood 8c Adolescent Immunization Schedules
242(29)
Vaccine Safety
242(8)
Vaccination in Special Circumstances
250(1)
Communicating with Parents About Vaccines
251(1)
Hepatitis B Vaccination
252(2)
Rotavirus Vaccination
254(1)
Diphtheria-Tetanus-Acellular Pertussis Vaccination
255(2)
Haemophilus Influenzae Type B Vaccination
257(1)
Pneumococcal Vaccination
258(2)
Poliomyelitis Vaccination
260(1)
Influenza Vaccination
261(1)
Measles, Mumps, & Rubella Vaccination
262(3)
Varicella Vaccination
265(1)
Hepatitis A Vaccination
266(1)
Meningococcal Vaccination
267(2)
Tetanus-Reduced Diphtheria-Acellular Pertussis Vaccination (Adolescents & Adults)
269(1)
Human Papillomavirus Vaccination
270(1)
Vaccinations for Special Situations
271(5)
Rabies Vaccination
271(1)
Typhoid Fever Vaccination
272(1)
Cholera Vaccination
273(1)
Japanese Encephalitis Vaccination
273(1)
Tuberculosis Vaccination
273(1)
Yellow Fever Vaccination
274(1)
Passive Prophylaxis
274(2)
11 Normal Childhood Nutrition & Its Disorders
276(29)
Matthew A. Haemer
Liliane K. Diab
Laura E. Primak
Nancy F. Krebs
Nutritional Requirements
276(8)
Nutrition & Growth
276(1)
Energy
276(1)
Protein
277(1)
Lipids
278(1)
Carbohydrates
279(1)
Major Minerals
280(1)
Trace Elements
280(1)
Vitamins
280(4)
Infant Feeding
284(8)
Breast-Feeding
284(7)
Special Dietary Products for Infants
291(1)
Nutrition for Children 2 Years & Older
292(5)
Pediatric Undernutrition
292(2)
Pediatric Overweight & Obesity
294(3)
Nutrition Support
297(8)
Enteral
297(1)
Parenteral Nutrition
298(1)
Nutrient Requirements & Delivery
299(6)
12 Emergencies & Injuries
305(23)
Jonathan Orsborn
Cortney Braund
Introduction to Pediatric Emergencies & Injuries
305(7)
Initial Approach to the Acutely
111(194)
Infant or Child
305(1)
The ABCs of Resuscitation
306(4)
Management of Shock
310(1)
Summary of Initial Approach to the Acutely III Infant or Child
311(1)
Emergency Pediatric Drugs
311(1)
Approach to the Pediatric Trauma Patient
312(5)
Mechanism of Injury
312(1)
Initial Assessment & Management
312(1)
Primary Survey
313(2)
Secondary Survey
315(2)
Head Injury
317(2)
Burns
319(2)
Thermal Burns
319(2)
Electrical Burns
321(1)
Disorders Due to Extremes of Environment
321(2)
Heat-Related Illnesses & Heat Stroke
321(1)
Hypothermia
322(1)
Submersion Injuries
323(1)
Lacerations
324(1)
Animal & Human Bites
325(1)
Dog Bites
325(1)
Cat Bites
326(1)
Human Bites
326(1)
Pain Management & Procedural Sedation
326(2)
13 Poisoning
328(29)
George Sam Wang
Barry H. Rumack
Richard C. Dart
Introduction
328(1)
Pharmacologic Principles of Toxicology
328(1)
Preventing Childhood Poisonings
329(1)
General Treatment of Poisoning
329(4)
Initial Telephone Contact
329(3)
Initial Emergency Department Contact
332(1)
Definitive Therapy of Poisoning
332(1)
Management of Specific Common Poisonings
333(3)
Acetaminophen (Paracetamol)
333(2)
Alcohol, Ethyl (Ethanol)
335(1)
Amphetamines & Related Drugs (Stimulants, Methamphetamine, 3,4-Methylenedioxy-N-Methylamphetamine)
336(1)
Anesthetics, Local
336(1)
Antihistamines & Cough & Cold Preparations
337(1)
Barbiturates & Benzodiazepines
338(1)
Belladonna Alkaloids (Atropine, Jimsonweed, Potato Leaves, Scopolamine, Stramonium)
338(1)
β-Blockers & Calcium Channel Blockers
338(1)
Carbon Monoxide
339(1)
Caustics
339(1)
Central α2-Adrenergic Agonist
340(1)
Cocaine
340(1)
Cosmetics & Related Products
341(1)
Cyclic Antidepressants
341(1)
Digitalis & Other Cardiac Glycosides
341(1)
Diphenoxylate with Atropine (Lomotil) & Loperamide (Imodium)
342(1)
Disinfectants & Deodorizers
342(1)
Disk-Shaped "Button" Batteries
343(1)
Ethylene Glycol & Methanol
343(1)
γ- Hydroxybutyrate, γ- Butyrolactone, Butanediol, Flunitrazepam, & Ketamine
344(1)
Hydrocarbons (Benzene, Charcoal Lighter Fluid, Gasoline, Kerosene, Petroleum Distillates, Turpentine)
344(1)
Ibuprofen
344(1)
Insect Stings (Bee, Wasp, & Hornet)
345(1)
Insecticides
345(1)
Iron
346(1)
Lead
346(1)
Magnets
347(1)
Marijuana
347(1)
Mushrooms
348(1)
Nitrites, Nitrates, Aniline, Pentachlorophenol, & Dinitrophenol
348(1)
Opioids & Opiates
349(1)
Oral Anti-Diabetics (Sulfonylureas, Metformin)
349(1)
Antipsychotics (Typical & Atypical)
350(1)
Plants
350(1)
Psychotropic Drugs
351(1)
Salicylates
352(1)
Scorpion Stings
353(1)
Serotonin Reuptake Inhibitors
353(1)
Snakebite
353(1)
Soaps & Detergents
354(1)
Spider Bites
355(1)
Vitamins
355(1)
Warfarin (Coumadin) & Newer Oral Anticoagulants (NOAC)
356(1)
14 Critical Care
357(36)
Amy C. Clevenger
Angela S. Czaja
Ryan J. Good
Cameron F. Gunville
D.O. Leslie A. Ridall
D.O. Todd C. Carpenter
Eva N. Grayck
Carleen Schneiter
Introduction
357(1)
Respiratory Critical Care
357(7)
Acute Respiratory Failure
357(4)
Conventional Mechanical Ventilation
361(2)
Other Modes of Respiratory Support
363(1)
Major Respiratory Diseases in the Pediatric ICU
364(6)
Acute Respiratory Distress Syndrome
364(4)
Status Asthmaticus
368(2)
Cardiovascular Critical Care
370(7)
Shock
370(3)
Sepsis
373(4)
Neurocritical Care
377(5)
Traumatic Brain Injury
377(3)
Hypoxic-Ischemic Encephalopathy
380(1)
Status Epilepticus
381(1)
Acute Kidney Injury & Renal Replacement Therapy
382(1)
Fluid Management & Nutritional Support of the Critically 111 Child
383(3)
Sedation & Analgesia in the Pediatric ICU
386(3)
End-of-Life Care & Death in the PICU
389(3)
Quality Improvement Initiatives in the PICU
392(1)
15 Skin
393(21)
Lori D. Prok
Carla X. Torres-Zegarra
General Principles
393(2)
Diagnosis of Skin Disorders
393(1)
Treatment of Skin Disorders
393(2)
Disorders of the Skin in Newborns
395(4)
Transient Diseases in Newborns
395(1)
Pigment Cell Birthmarks, Nevi, & Melanoma
396(1)
Melanocyte Nevi
396(1)
Vascular Birthmarks
397(1)
Epidermal Birthmarks
398(1)
Connective Tissue Birthmarks (Juvenile Elastoma, Collagenoma)
399(1)
Hereditary Skin Disorders
399(1)
Common Skin Diseases in Infants, Children, & Adolescents
399(1)
Acne
399(3)
Bacterial Infections of the Skin
402(1)
Fungal Infections of the Skin
403(1)
Viral Infections of the Skin
404(1)
Virus-Induced Tumors
405(1)
Insect Infestations
406(1)
Dermatitis (Eczema)
406(3)
Common Skin Tumors
409(1)
Papulosquamous Eruptions
410(1)
Hair Loss (Alopecia)
411(1)
Reactive Erythemas
412(1)
Miscellaneous Skin Disorders Seen in Pediatric Practice
413(1)
16 Eye
414(45)
Jennifer Lee Jung
Introduction
414(1)
Common Nonspecific Signs & Symptoms
414(1)
Red Eye
414(1)
Tearing
414(1)
Discharge
414(1)
Pain & Foreign-Body Sensation
414(1)
Photophobia
414(1)
Abnormal Red Reflex
414(1)
Refractive Errors
415(1)
Myopia (Nearsightedness)
416(1)
Hyperopia (Farsightedness)
416(1)
Astigmatism
416(1)
Ophthalmic Examination
416(4)
History
416(1)
Visual Acuity
416(1)
External Examination
417(1)
Pupils
418(1)
Alignment & Motility Evaluation
418(1)
Ophthalmoscopic Examination
419(1)
Ocular Trauma
420(5)
Prevention of Ocular Injuries
420(1)
Corneal Abrasion
420(1)
Ocular Foreign Bodies
420(1)
Intraocular Foreign Bodies & Perforating Ocular Injuries
421(1)
Blunt Orbital Trauma
422(1)
Lacerations
423(1)
Burns
423(1)
Hyphema
424(1)
Abusive Head Trauma & Nonaccidental Trauma
425(1)
Disorders of the Ocular Structures
425(5)
Diseases of the Eyelids
425(3)
Viral Eyelid Disease
428(1)
Miscellaneous Eyelid Infections
428(1)
Eyelid Ptosis
428(1)
Horner Syndrome
429(1)
Eyelid Tics
430(1)
Disorders of the Nasolacrimal System
430(2)
Nasolacrimal Duct Obstruction
430(1)
Congenital Dacryocystocele
431(1)
Dacryocystitis
431(1)
Diseases of the Conjunctiva
432(5)
Ophthalmia Neonatorum
432(1)
Bacterial Conjunctivitis
433(1)
Viral Conjunctivitis
434(1)
Allergic Conjunctivitis
435(1)
Mucocutaneous Diseases
435(2)
Disorders of the Iris
437(2)
Iris Coloboma
437(1)
Aniridia
437(1)
Albinism
438(1)
Miscellaneous Iris Conditions
438(1)
Glaucoma
439(1)
Uveitis
439(3)
Anterior Uveitis/Iridocyclitis/Iritis
439(1)
Posterior Uveitis
440(1)
Intermediate Uveitis
441(1)
Disorders of the Cornea
442(1)
Cloudy Cornea
442(1)
Viral Keratitis
442(1)
Corneal Ulcers
443(1)
Disorders of the Lens
443(2)
Cataracts
444(1)
Dislocated Lenses/Ectopia Lentis
444(1)
Disorders of the Retina
445(3)
Retinal Hemorrhages in the Newborn
445(1)
Retinopathy of Prematurity (ROP)
445(1)
Retinoblastoma
446(1)
Retinal Detachment
447(1)
Diabetic Retinopathy
447(1)
Diseases of the Optic Nerve
448(4)
Optic Neuropathy
448(1)
Optic Nerve Hypoplasia
448(1)
Papilledema
449(1)
Optic Neuritis
450(1)
Optic Atrophy
451(1)
Diseases of the Orbit
452(3)
Periorbital & Orbital Cellulitis
452(1)
Craniofacial Anomalies
452(1)
Orbital Tumors
453(1)
Nystagmus
453(1)
Amblyopia
454(1)
Strabismus
455(1)
Esotropia (Crossed Eyes)
455(1)
Exotropia (Wall-Eyed, Drifting of Eyes)
456(3)
Unexplained Decreased Vision in Infants & Children
457(1)
Learning Disabilities & Dyslexia
458(1)
17 Oral Medicine & Dentistry
459(12)
Roopa P. Gandhi
Chaitanya P. Puranik
Anne Wilson
Katherine L. Chin
Pediatric Oral Health
459(1)
Oral Examination of Children
460(3)
Dental Caries
463(3)
Periodontal Disease
466(1)
Dental Emergencies
466(3)
Special Patient Populations
469(1)
Orthodontic Referral
470(1)
18 Ear, Nose, & Throat
471(28)
Patricia J. Yoon
Melissa A. Scholes
Brian W. Herrmann
The Ear
471(13)
Infections of the Ear
471(9)
Acute Trauma to the Middle Ear
480(1)
Ear Canal Foreign Body & Cerumen Impaction
481(1)
Auricular Hematoma
481(1)
Congenital Ear Malformations
481(1)
Identification & Management of Hearing Loss
482(2)
The Nose & Paranasal Sinuses
484(6)
Acute Viral Rhinitis
484(2)
Rhinosinusitis
486(2)
Choanal Atresia
488(1)
Recurrent Rhinitis
488(1)
Epistaxis
488(1)
Nasal Infection
489(1)
Nasal Trauma
489(1)
Foreign Bodies in the Nose
489(1)
The Throat & Oral Cavity
490(9)
Acute Stomatitis
490(1)
Pharyngitis
490(3)
Peritonsillar Cellulitis or Abscess (Quinsy)
493(1)
Retropharyngeal Abscess
494(1)
Ludwig Angina
494(1)
Acute Cervical Adenitis
494(1)
Tonsillectomy & Adenoidectomy
495(1)
Disorders of the Lips
496(1)
Disorders of the Tongue
496(1)
Halitosis
497(1)
Salivary Gland Disorders
497(1)
Congenital Oral Malformations
497(2)
19 Respiratory Tract & Mediastinum
499(52)
Monica J. Federico
Christopher D. Baker
Emily M. DeBoer
Oren Kupfer
Stacey L. Martiniano
Paul Stillwell
Stephen Hawkins
Deborah Liptzin
Respiratory Tract
499(1)
Growth & Development
499(1)
Diagnostic Aids
499(5)
Physical Examination of the Respiratory Tract
499(1)
Pulmonary Function Tests
500(1)
Assessment of Oxygenation & Ventilation
501(1)
Diagnosis of Respiratory Tract Infections
502(2)
Imaging of the Respiratory Tract
504(1)
Laryngoscopy & Bronchoscopy
504(1)
General Therapy for Pediatric Lung Diseases
504(2)
Oxygen Therapy
504(1)
Inhalation of Medications
505(1)
Airway Clearance Therapy
506(1)
Avoidance of Environmental Hazards
506(1)
Disorders of the Conducting Airways
506(1)
Laryngomalacia & Congenital Disorders of the Extrathoracic Airway
507(1)
Laryngomalacia
507(1)
Other Causes of Congenital Extrathoracic Obstruction
507(1)
Acquired Disorders of the Extrathoracic Airway
508(4)
Foreign-Body Aspiration in the Extrathoracic Airway
508(1)
Croup Syndromes
509(2)
Vocal Fold Immobility
511(1)
Subglottic Stenosis
511(1)
Congenital Causes of Intrathoracic Airway Obstruction
512(1)
Malacia of Airways
512(1)
Vascular Rings & Slings
512(1)
Bronchogenic Cysts
513(1)
Acquired Causes of Intrathoracic Airway Obstruction
513(1)
Foreign-Body Aspiration in the Intrathoracic Airway
514(1)
Disorders of Mucociliary Clearance
514(4)
Cystic Fibrosis
514(2)
Primary Ciliary Dyskinesia
516(1)
Bronchiectasis
517(1)
Congenital Malformations of the Lung Parenchyma
518(3)
Pulmonary Agenesis & Hypoplasia
518(1)
Pulmonary Sequestration
519(1)
Congenital Lobar Overinflation
519(1)
Congenital Pulmonary Airway Malformation (Previously Named Cystic Adenomatoid Malformation)
520(1)
Acquired Abnormalities of the Lung Parenchyma
521(5)
Bronchopulmonary Dysplasia
521(2)
Community-Acquired Bacterial Pneumonia
523(2)
Parapneumonic Effusion & Empyema
525(1)
Atypical Pneumonias
526(6)
Viral Pneumonia
526(1)
Bronchiolitis
527(1)
Mycoplasma Pneumonia
528(1)
Aspiration Pneumonia
528(1)
Pneumonia in the Immunocompromised Host
529(2)
Lung Abscess
531(1)
Bronchiolitis Obliterans
532(3)
Children's Interstitial Lung Disease Syndrome
533(2)
Hypersensitivity Pneumonitis
535(1)
Diseases of the Pulmonary Circulation
535(4)
Pulmonary Hemorrhage
535(2)
Pulmonary Embolism
537(1)
Pulmonary Edema
538(1)
Congenital Pulmonary Lymphangiectasia
539(1)
Disorders of the Chest Wall
539(1)
Scoliosis
539(1)
Pectus Carinatum
539(1)
Pectus Excavatum
540(1)
Neuromuscular Disorders & Lung Disease
540(1)
Disorders of the Pleura & Pleural Cavity
540(2)
Hemothorax
541(1)
Chylothorax
541(1)
Pneumothorax & Related Air Leak Syndromes
542(1)
Mediastinum
542(1)
Mediastinal Masses
542(1)
Sleep-Disordered Breathing
543(1)
Primary Snoring & Obstructive Sleep Apnea
544(2)
Periodic Breathing & Central Sleep Apnea
546(1)
Brief Resolved Unexplained Events (Formerly Apparent Life-Threatening Events)
546(5)
Sudden Unexpected Infant Death & Sudden Infant Death Syndrome
549(1)
Quality Assessment & Outcomes Metrics
550(1)
20 Cardiovascular Diseases
551(64)
Pei-Ni Jone
John S. Kim
Johannes von Alvensleben
Dale Burkett
Introduction
551(1)
Diagnostic Evaluation
551(9)
History
551(1)
Physical Examination
551(3)
Electrocardiography
554(2)
Chest Radiograph
556(1)
Echocardiography
557(1)
Magnetic Resonance Imaging
558(1)
Cardiopulmonary Stress Testing
558(1)
Arterial Blood Gases & Pulse Oximetry
558(1)
Cardiac Catheterization & Angiocardiography
559(1)
Perinatal & Neonatal Circulation
560(1)
Heart Failure
561(2)
Genetic Basis of Congenital Heart Disease
563(1)
Acyanotic Congenital Heart Disease
564(14)
Defects in Septation
564(4)
Patent (Persistent) Ductus Arteriosus
568(1)
Right-Sided Obstructive Lesions
569(3)
Left-Sided Lesions
572(4)
Diseases of the Aorta
576(1)
Coronary Artery Abnormalities
577(1)
Cyanotic Congenital Heart Disease
578(10)
Tetralogy of Fallot
578(2)
Pulmonary Atresia with Ventricular Septal Defect
580(1)
Pulmonary Atresia with Intact Ventricular Septum
580(1)
Tricuspid Atresia
581(1)
Hypoplastic Left Heart Syndrome
582(2)
Transposition of the Great Arteries
584(1)
Total Anomalous Pulmonary Venous Return
585(2)
Truncus Arteriosus
587(1)
Quality Improvement in Congenital Heart Disease
588(1)
Acquired Heart Disease
588(10)
Rheumatic Fever
588(2)
Kawasaki Disease
590(1)
Infective Endocarditis
591(2)
Pericarditis
593(1)
Cardiomyopathy
594(3)
Myocarditis
597(1)
Preventive Cardiology
598(1)
Hypertension
598(1)
Atherosclerosis & Dyslipidemias
598(1)
Chest Pain
599(1)
Cardiac Transplantation
600(1)
Quality Improvement for Pediatric Heart Transplantation
601(1)
Pulmonary Hypertension
602(1)
Disorders of Rate & Rhythm
603(9)
Disorders of the Sinus Node
603(1)
Premature Beats
604(1)
Supraventricular Tachycardia
605(4)
Ventricular Tachycardia
609(1)
Long QT Syndrome
609(1)
Sudden Cardiac Death
610(1)
Disorders of Atrioventricular Conduction
610(2)
Syncope (Fainting)
612(3)
Introduction
612(1)
Diagnostic Evaluation
612(1)
Vasovagal/Neurocardiogenic Syncope
613(2)
21 Gastrointestinal Tract
615(42)
David Brumbaugh
Glenn T. Furuta
Edward J. Hoffenberg
Gregory E. Kobak
Robert E. Kramer
Seth Septer
MaryShull
Jason Soden
Thomas Walker
Disorders of the Esophagus
615(6)
Gastroesophageal Reflux & GERD
615(2)
Eosinophilic Esophagitis
617(1)
Achalasia of the Esophagus
618(1)
Caustic Burns of the Esophagus
619(1)
Foreign Bodies in the Alimentary Tract
620(1)
Disorders of the Stomach & Duodenum
621(4)
Hiatal & Paraesophageal Hernia
621(1)
Pyloric Stenosis
622(1)
Gastric & Duodenal Ulcer
623(1)
Congenital Diaphragmatic Hernia
624(1)
Congenital Duodenal Obstruction
624(1)
Disorders of the Small Intestine
625(6)
Intestinal Atresia & Stenosis
625(1)
Intestinal Malrotation
626(1)
Short Bowel Syndrome
627(1)
Intussusception
628(1)
Inguinal Hernia
629(1)
Umbilical Hernia
629(1)
Patent Omphalomesenteric Duct
630(1)
Meckel Diverticulum
630(1)
Acute Appendicitis
630(1)
Duplications of the Gastrointestinal Tract
631(1)
Disorders of the Colon
631(5)
Congenital Aganglionic Megacolon (Hirschsprung Disease)
631(2)
Constipation
633(1)
Anal Fissure
634(1)
Congenital Anorectal Anomalies
634(1)
Clostridium Difficile Infection in Children
635(1)
Disorders of the Peritoneal Cavity
636(1)
Peritonitis
636(1)
Chylous Ascites
637(1)
Gastrointestinal Tumors & Malignancies
637(3)
Juvenile Polyps
637(1)
Cancers of the Esophagus, Small Bowel, & Colon
638(1)
Mesenteric Cysts
638(1)
Intestinal Hemangiomas & Vascular Malformations
639(1)
Major Gastrointestinal Symptoms & Signs
640(17)
Acute Diarrhea
640(1)
Chronic Diarrhea
641(2)
Gastrointestinal Bleeding
643(3)
Vomiting
646(1)
Abdominal Pain
647(2)
Acute Abdomen
649(1)
Malabsorption Syndromes
649(4)
Inflammatory Bowel Disease
653(4)
22 Liver & Pancreas
657(47)
Ronald J. Sokol
Michael R. Narkewicz
Jacob A. Mark
Cara L. Mack
Amy G. Feldman
Shikha S. Sundaram
Liver Disorders
657(39)
Neonatal Cholestatic Jaundice
657(1)
Intrahepatic Cholestasis
657(9)
Extrahepatic Neonatal Cholestasis
666(2)
Other Neonatal Hyperbilirubinemic Conditions (Noncholestatic Nonhemolytic)
668(3)
Hepatitis A
671(2)
Hepatitis B
673(1)
Hepatitis C
674(2)
Hepatitis D (Delta Agent)
676(1)
Hepatitis E
676(1)
Other Hepatitis Viruses
676(1)
Acute Liver Failure
676(2)
Autoimmune Hepatitis
678(1)
Nonalcoholic Fatty Liver Disease
679(1)
α1,-Antitrypsin Deficiency Liver Disease
680(2)
Wilson Disease (Hepatolenticular Degeneration)
682(1)
Drug-Induced Liver Diseases
683(1)
Cirrhosis
684(1)
Portal Hypertension
685(3)
Biliary Tract Disease
688(5)
Pyogenic & Amebic Liver Abscess
693(1)
Liver Tumors
694(1)
Liver Transplantation
695(1)
Pancreatic Disorders
696(8)
Acute Pancreatitis
696(1)
Chronic Pancreatitis
697(1)
Gastrointestinal & Hepatobiliary Manifestations of Cystic Fibrosis
698(3)
Syndromes with Pancreatic Exocrine Insufficiency
701(1)
Isolated Exocrine Pancreatic Enzyme Defect
701(1)
Pancreatic Tumors
702(1)
References
703(1)
23 Fluid, Electrolyte, & Acid-Base Disorders & Therapy
704(10)
Melisha G. Hanna
Margret E. Bock
Regulation of Body Fluids, Electrolytes, & Tonicity
704(1)
Acid-Base Balance
705(1)
Fluid & Electrolyte Management
706(6)
Dehydration
707(2)
Hyponatremia
709(1)
Hypernatremia
710(1)
Potassium Disorders
710(2)
Acid-Base Disturbances
712(2)
Metabolic Acidosis
712(1)
Metabolic Alkalosis
712(1)
Respiratory Acidosis
713(1)
Respiratory Alkalosis
713(1)
24 Kidney & Urinary Tract
714(26)
Margret E. Bock
Melisha G. Hanna
Evaluation of the Kidney & Urinary Tract
714(4)
History
714(1)
Physical Examination
714(1)
Laboratory Evaluation of Renal Function
714(4)
Laboratory Evaluation of Immunologic Function
718(1)
Radiographic Evaluation
718(1)
Renal Biopsy
718(1)
Congenital Anomalies of the Urinary Tract
718(2)
Renal Parenchymal Anomalies
718(2)
Distal Urinary Tract Anomalies
720(1)
Hematuria & Glomerular Disease
720(2)
Microhematuria
720(1)
Glomerulonephritis
721(1)
Tubulointerstitial Disease
722(1)
Acute Interstitial Nephritis
722(1)
Proteinuria & Renal Disease
723(2)
Congenital Nephrosis (Finnish Type)
723(1)
Idiopathic Nephrotic Syndrome of Childhood
723(1)
Focal Segmental Glomerulosclerosis
724(1)
Membranous Nephropathy (Membranous Glomerulonephritis)
724(1)
Diseases of the Renal Vessels
725(1)
Renal Vein Thrombosis
725(1)
Renal Arterial Disease
725(1)
Hemolytic-Uremic Syndrome
725(1)
Renal Failure
726(4)
Acute Kidney Injury
726(3)
Chronic Renal Failure
729(1)
Hypertension
730(3)
Inherited or Developmental Defects of the Kidneys
733(4)
Disorders of the Renal Tubules
733(2)
Cystinosis
735(1)
Oculocerebrorenal Syndrome (Lowe Syndrome)
735(1)
Hypokalemic Alkalosis (Bartter Syndrome, Gitelman Syndrome, & Liddle Syndrome)
735(1)
Nephrogenic Diabetes Insipidus
736(1)
Nephrolithiasis
736(1)
Urinary Tract Infections
737(2)
QA/QI in Pediatric Nephrology
739(1)
25 Neurologic & Muscular Disorders
740(71)
Ricka Messer
Teri L. Schreiner
Diana Walleigh
Michele L. Yang
Jan A. Martin
Scott Demarest
Neurologic Assessment & Neurodiagnostics
740(6)
History & Examination
740(1)
Diagnostic Testing
740(2)
Pediatric Neuroradiologic Procedures
742(4)
Disorders Affecting the Nervous System in Infants & Children
746(34)
Altered States of Consciousness (Coma)
746(2)
Seizures & Epilepsy
748(12)
Sleep Disorders
760(1)
Headaches
761(3)
Pseudotumor Cerebri (Idiopathic Intracranial Hypertension)
764(2)
Cerebrovascular Disease
766(3)
Congenital Malformations of the Nervous System
769(3)
Abnormal Head Size
772(2)
Neurocutaneous Dysplasias
774(6)
Central Nervous System Degenerative Disorders of Infancy & Childhood
780(1)
Ataxias of Childhood
780(7)
Acute Ataxias of Childhood
780(3)
Chronic & Episodic Ataxias
783(1)
Movement Disorders
783(3)
Cerebral Palsy
786(1)
Infections & Inflammatory Disorders of the Central Nervous System
787(5)
Bacterial Meningitis
788(1)
Brain Abscess
789(1)
Viral Infections
790(1)
Encephalopathy of Human Immunodeficiency Virus Infection
790(1)
Other Infections
790(1)
Noninfectious Inflammatory Disorders of the Central Nervous System
790(2)
Syndromes Presenting as Acute Flaccid Weakness
792(15)
Disorders of Childhood Affecting Muscles
796(6)
Benign Acute Childhood Myositis
802(1)
Disorders of Neuromuscular Transmission
802(3)
Lesions of the Peripheral Nerve
805(1)
Peripheral Neuropathy
806(1)
Motor Neuron Disorders
807(1)
Miscellaneous Neuromuscular Disorders
808(3)
Floppy Infant Syndrome
808(3)
26 Orthopedics
811(26)
Jason T. Rhodes
Alex Tagawa
Cameron Niswander
Wade Coomer
Mark A. Erickson
Sayan De
Introduction
811(1)
Disturbances of Prenatal Origin
811(1)
Congenital Amputations & Limb Deficiencies
811(1)
Deformities of the Extremities
812(6)
Common Foot Problems
812(2)
Genu Varum & Genu Valgum
814(1)
Tibial Torsion & Femoral Anteversion
815(1)
Developmental Dysplasia of the Hip Joint
815(2)
Slipped Capital Femoral Epiphysis
817(1)
Common Spine Conditions
818(3)
Back Pain
818(1)
Torticollis
818(1)
Scoliosis
819(1)
Kyphosis
820(1)
Inflammatory Conditions
821(1)
Syndromes with Musculoskeletal Involvement
821(3)
Arthrogryposis Multiplex Congenita (Amyoplasia Congenita)
821(2)
Neurologic Disorders Involving the Musculoskeletal System
823(1)
Trauma
824(2)
Traumatic Subluxations & Dislocations
825(1)
Fractures
826(2)
Infections of the Bones & Joints
828(3)
Vascular Lesions & Avascular Necrosis (Osteochondroses)
831(2)
Neoplasia of the Musculoskeletal System
833(1)
Miscellaneous Diseases of Bone & Joint
834(2)
Fibrous Dysplasia
835(1)
Bone Cysts, Baker Cyst, & Ganglions
835(1)
Quality Assurance/Improvement Initiatives in Orthopedics
836(1)
27 Sports Medicine
837(29)
Katherine S. Dahab
Stephanie W. Mayer
Kyle B. Nagle
Armando Vidal
Basic Principles
837(9)
Fitness & Conditioning
837(1)
Sports Nutrition
838(1)
Preparticipation Physical Evaluation
838(7)
Rehabilitation of Sports Injuries
845(1)
Common Sports Medicine Issues & Injuries
846(18)
Infectious Diseases
846(1)
Head & Neck Injuries
847(3)
Spine Injuries
850(1)
Shoulder Injuries
851(2)
Elbow Injuries
853(2)
Hand & Wrist Injuries
855(2)
Hip Injuries
857(2)
Knee Injuries
859(4)
Foot & Ankle Injuries
863(1)
Prevention
864(2)
28 Rehabilitation Medicine
866(9)
Pamela E. Wilson
Gerald H. Clayton
Pediatric Brain Injury
866(3)
Spinal Cord Injury
869(2)
Brachial Plexus Lesions & Typical Features
871(1)
Common Rehabilitation Problems
872(2)
Quality Assurance/Improvement Initiatives in Rehabilitation Medicine
874(1)
29 Rheumatic Diseases
875(9)
Jennifer B. Soep
Juvenile Idiopathic Arthritis
875(3)
Systemic Lupus Erythematosus
878(2)
Dermatomyositis
880(1)
Vasculitis
881(1)
Raynaud Phenomenon
882(1)
Noninflammatory Pain Syndromes
882(2)
30 Hematologic Disorders
884(55)
Michael Wang
Christopher McKinney
Rachelle Nuss
Daniel R. Ambruso
Normal Hematologic Values
884(1)
Bone Marrow Failure
884(1)
Constitutional Aplastic Anemia (Fanconi Anemia)
884(2)
Acquired Aplastic Anemia
886(1)
Anemias
887(18)
Approach to the Child with Anemia
887(1)
Pure Red Cell Aplasia
888(2)
Nutritional Anemias
890(2)
Anemia of Chronic Disorders
892(1)
Congenital Hemolytic Anemias: Red Cell Membrane Defects
893(2)
Congenital Hemolytic Anemias: Hemoglobinopathies
895(6)
Congenital Hemolytic Anemias: Disorders of Red Cell Metabolism
901(2)
Acquired Hemolytic Anemia
903(2)
Polycythemia & Methemoglobinemia
905(1)
Methemoglobinemia
906(1)
Disorders of Leukocytes
906(22)
Neutropenia
906(2)
Neutrophilia
908(1)
Disorders of Neutrophil Function
909(2)
Lymphocytosis
911(1)
Eosinophilia
911(1)
Bleeding Disorders
912(1)
Abnormalities of Platelet Number or Function
913(4)
Inherited Bleeding Disorders
917(4)
Von Willebrand Disease
921(1)
Acquired Bleeding Disorders
922(2)
Vascular Abnormalities Associated with Bleeding
924(1)
Thrombotic Disorders
925(3)
Splenic Abnormalities
928(2)
Splenomegaly & Hypersplenism
928(1)
Asplenia & Splenectomy
928(2)
Transfusion Medicine
930(9)
Donor Screening & Blood Processing: Risk Management
930(1)
Storage & Preservation of Blood & Blood Components
931(1)
Pretransfusion Testing
931(4)
Transfusion Practice
935(3)
References
938(1)
31 Neoplastic Disease
939(34)
Amy K. Keating
Jessica Knight-Perry
Kelly Moloney
Jean M. Mulcahy Levy
Brian S. Greffe
Anna R. K. Franklin
Timothy Price Garrington
Major Pediatric Neoplastic Diseases
939(28)
Acute Lymphoblastic Leukemia
939(3)
Acute Myeloid Leukemia
942(3)
Myeloproliferative Diseases
945(1)
Brain Tumors
946(4)
Lymphomas & Lymphoproliferative Disorders
950(5)
Neuroblastoma
955(3)
Wilms Tumor (Nephroblastoma)
958(1)
Bone Tumors
959(2)
Rhabdomyosarcoma
961(2)
Retinoblastoma
963(1)
Hepatic Tumors
964(2)
Langerhans Cell Histiocytosis
966(1)
Blood & Marrow Transplant & Cellular Therapeutics
967(2)
General Considerations
967(1)
BMT Complications
968(1)
Cellular Therapeutics
968(1)
Late Effects of Pediatric Cancer Therapy
969(4)
Growth Complications
970(1)
Endocrine Complications
970(1)
Cardiopulmonary Complications
971(1)
Renal Complications
971(1)
Neuropsychological Complications
971(1)
Second Malignancies
971(2)
32 Pain Management & Pediatric Palliative & End-of-Life Care
973(11)
Brian S. Greffe
Jeffrey L. Galinkin
Nancy A. King
Introduction
973(5)
Pain Assessment
973(1)
Acute Pain
973(2)
Chronic Pain Management
975(3)
Pediatric Palliative & End-of-Life Care
978(6)
Introduction
978(1)
Children Who May Benefit From Palliative Care Interventions
978(1)
Pain Management in Pediatric Palliative Care
979(1)
Quality-of-Life Adjuncts & Symptom Management in Pediatric Palliative Care
979(1)
Psychosocial Aspects of Pediatric Palliative Care
979(1)
Children's Concept of Death
980(1)
Spiritual & Cultural Support
981(1)
Withdrawal of Medical Life Support
982(1)
Advance Care Planning
982(1)
References
983(1)
33 Immunodeficiency
984(19)
Jordan K. Abbott
Pia J. Hauk
Introduction
984(1)
Immunodeficiency Evaluation: Primary Considerations
984(4)
Severe Combined Immunodeficiency Diseases
988(2)
SCID Classification
990(1)
Other Combined Immunodeficiencies
990(3)
Antibody Deficiency Syndromes
993(3)
Phagocyte Disorders
996(2)
Deficiencies of the Innate Immune System
998(1)
Immunodeficiency Diseases That Present with Autoimmunity
999(1)
Immunodeficiency Diseases That Overlap with Allergy
1000(3)
34 Endocrine Disorders
1003(39)
Sarah Bartz
Christina Chambers
Christine M. Chan
Melanie Cree-Green
Shanlee Davis
Stephanie Hsu
General Concepts
1003(1)
Hormone Types
1003(1)
Feedback Control of Hormone Secretion
1003(1)
Disturbances of Growth
1004(8)
Target Height & Skeletal Maturation
1005(1)
Short Stature
1005(6)
Tall Stature
1011(1)
Disorders of the Posterior Pituitary Gland
1012(1)
Arginine Vasopressin (Antidiuretic Hormone) Physiology
1012(1)
Central Diabetes Insipidus
1012(1)
Thyroid Gland
1013(5)
Fetal Development of the Thyroid
1013(1)
Physiology
1013(1)
Hypothyroidism (Congenital & Acquired)
1013(2)
Thyroiditis
1015(1)
Hyperthyroidism
1016(2)
Thyroid Cancer
1018(1)
Disorders of Calcium & Phosphorus Metabolism
1018(7)
Hypocalcemic Disorders
1018(4)
Pseudohypoparathyroidism (Resistance to Parathyroid Hormone Action)
1022(1)
Hypercalcemic States
1022(2)
Familial Hypocalciuric Hypercalcemia (Familial Benign Hypercalcemia)
1024(1)
Hypervitaminosis D
1024(1)
Williams Syndrome
1024(1)
Immobilization Hypercalcemia
1024(1)
Hypophosphatasia
1024(1)
Gonads (Ovaries & Testes)
1025(2)
Development
1025(1)
Disorders of Sexual Development
1025(2)
Abnormalities in Female Pubertal Development & Ovarian Function
1027(3)
Polycystic Ovarian Syndrome
1030(1)
Abnormalities in Male Pubertal Development & Testicular Function
1031(2)
Adrenal Cortex
1033(2)
Adrenocortical Insufficiency
1034(1)
Congenital Adrenal Hyperplasias
1035(2)
Adrenocortical Hyperfunction
1037(1)
Primary Hyperaldosteronism
1038(1)
Uses of Glucocorticoids & Adrenocorticotropic Hormone in Treatment of Nonendocrine Diseases
1039(3)
Adrenal Medulla Pheochromocytoma
1040(2)
35 Diabetes Mellitus
1042(13)
Brigitte I. Frohnert
Peter H. Chase
Marian Rewers
Quality Assessment & Outcomes Metrics
1049(4)
Associated Autoimmune Diseases in Type 1 Diabetes
1053(1)
Associated Conditions with Type 2 Diabetes
1054(1)
References
1054(1)
36 Inborn Errors of Metabolism
1055(26)
Janet A. Thomas
Johan L. K. Van Hove
Austin A. Larson
Peter R. Baker
Introduction
1055(1)
Diagnosis
1055(2)
Suspecting Inborn Errors
1055(1)
Laboratory Studies
1056(1)
Common Clinical Situations
1056(1)
Management of Metabolic Emergencies
1057(1)
Newborn Screening
1057(1)
Disorders of Carbohydrate Metabolism
1058(2)
Glycogen Storage Diseases
1058(1)
Galactosemia
1059(1)
Hereditary Fructose Intolerance
1060(1)
Disorders of Energy Metabolism
1060(3)
Disorders of Amino Acid Metabolism
1063(5)
Disorders of the Urea Cycle
1063(1)
Phenylketonuria & the Hyperphenylalaninemias
1064(2)
Hereditary Tyrosinemia
1066(1)
Maple Syrup Urine Disease (Branched-Chain Ketoaciduria)
1066(1)
Homocystinuria
1067(1)
Nonketotic Hyperglycinemia
1067(1)
Organic Acidemias
1068(3)
Propionic & Methylmalonic Acidemia (Ketotic Hyperglycinemias)
1068(2)
Carboxylase Deficiency
1070(1)
Glutaric Acidemia Type I
1070(1)
Disorders of Fatty Acid Oxidation & Carnitine
1071(1)
Fatty Acid Oxidation Disorders
1071(1)
Carnitine
1072(1)
Purine Metabolism Disorders
1072(1)
Lysosomal Diseases
1073(3)
Peroxisomal Diseases
1076(1)
Congenital Disorders of Glycosylation
1077(1)
Smith-Lemli-Opitz Syndrome & Disorders of Cholesterol Synthesis
1077(1)
Disorders of Brain Specific Metabolism: Neurotransmitters, Synthesis of Amino Acids & Glucose Transport
1078(1)
Creatine Synthesis Disorders
1079(1)
Quality Initiatives in the Field of Metabolic Disease
1080(1)
37 Genetics & Dysmorphology
1081(31)
Naomi J. L. Meeks
Margarita Saenz
Anne Chun-Hui Tsai
Ellen R. Bias
Foundations of Genetic Diagnosis
1081(6)
Cytogenetics
1081(4)
Molecular Genetics
1085(2)
Principles of Inherited Human Disorders
1087(5)
Mendelian Inheritance
1087(3)
Multifactorial Inheritance
1090(1)
Nonmendelian Inheritance
1091(1)
Family History & Pedigree
1092(1)
Dysmorphology & Human Embryology
1092(2)
Mechanisms
1093(1)
Clinical Dysmorphology
1093(1)
Chromosomal Disorders: Abnormal Number
1094(2)
Trisomies
1094(1)
Sex Chromosome Abnormalities
1095(1)
Chromosomal Abnormalities: Abnormal Structure
1096(1)
Chromosome Deletion Disorders
1097(1)
Contiguous Gene Disorders
1097(1)
Mendelian Disorders
1098(4)
Autosomal Dominant Disorders
1098(2)
Autosomal Recessive Disorders
1100(2)
X-Linked Disorders
1102(1)
Nonmendelian Disorders
1102(2)
Disorders of Imprinting
1102(1)
Disorders Associated with Anticipation
1103(1)
Disorders of Multifactorial Inheritance
1104(2)
Cleft Lip & Cleft Palate
1104(1)
Neural Tube Defects
1105(1)
Common Recognizable Disorders with Variable or Unknown Cause
1106(2)
Genetic Evaluation of the Child with Developmental Disabilities
1108(1)
Perinatal Genetics
1109(3)
Teratogens
1109(1)
Assisted Reproduction
1110(1)
Prenatal Diagnosis
1110(2)
38 Allergic Disorders
1112(40)
Ronina A. Covar
David M. Fleischer
Christine Cho
Mark Boguniewicz
Introduction
1112(1)
Asthma
1112(20)
Allergic Rhinoconjunctivitis
1132(4)
Atopic Dermatitis
1136(5)
Urticaria & Angioedema
1141(2)
Anaphylaxis
1143(2)
Adverse Reactions to Drugs & Biologicals
1145(3)
Food Allergy
1148(2)
Insect Allergy
1150(2)
39 Antimicrobial Therapy
1152(26)
Sarah K. Parker
Jason Child
Christine E. MacBrayne
Andrew Haynes
Justin Seams
Principles of Antimicrobial Therapy
1152(1)
Concepts for Judicious Use of Antimicrobials
1152(2)
Susceptibility Testing & Drug Dosing Properties
1154(1)
Pharmacodynamic Concepts
1154(1)
Use of Antimicrobial Agents to Prevent Disease
1155(1)
Choice of Antimicrobial Agents
1155(1)
Specific Antimicrobial Agents
1155(17)
β-Lactam Antibiotics
1155(1)
β-Lactam: Penicillins
1156(14)
β-Lactam: Cephalosporins
1170(2)
β-Lactam: Monobactams
1172(1)
β-Lactam: Carbapenems
1172(1)
Glycopeptide Agents
1172(1)
Daptomycin
1173(1)
Trimethoprim/Sulfamethoxazole
1173(1)
Metronidazole
1173(1)
Macrolides
1173(1)
Lincosamides
1174(1)
Oxazolidinones
1174(1)
Tetracyclines
1174(1)
Aminoglycosides
1175(1)
Rifamycins
1175(1)
Fluoroquinolones
1176(1)
Antifungals
1176(1)
Antivirals
1177(1)
References
1177(1)
40 Infections: Viral & Rickettsial
1178(46)
Daniel Olson
Myron J. Levin
Edwin J. Asturias
Viral Infections
1178(1)
Respiratory Infections
1178(12)
Viruses Causing the Common Cold
1178(3)
Infections Due to Adenoviruses
1181(3)
Influenza
1184(2)
Parainfluenza (Croup)
1186(1)
Respiratory Syncytial Virus Disease
1187(1)
Human Metapneumovirus Infection
1188(1)
Infections Due to Human Coronaviruses
1189(1)
Infections Due to Enteroviruses & Parechoviruses
1190(4)
Acute Febrile Illness
1190(1)
Respiratory Tract Illnesses
1190(1)
Rashes (Including Hand-Foot-&-Mouth Disease)
1191(1)
Central Nervous System Illnesses
1192(2)
Infections Due to Herpesviruses
1194(11)
Herpes Simplex Infections
1194(3)
Varicella & Herpes Zoster
1197(3)
Roseola Infantum (Exanthem Subitum)
1200(1)
Cytomegalovirus Infections
1201(3)
Infectious Mononucleosis (Epstein-Barr Virus)
1204(1)
Viral Infections Spread by Insect Vectors
1205(8)
Encephalitis
1209(1)
Dengue
1209(1)
Chikungunya
1210(1)
Zika
1211(1)
Colorado Tick Fever
1212(1)
Other Major Viral Childhood Exanthems
1213(4)
Erythema Infectiosum
1213(1)
Measles (Rubeola)
1214(2)
Rubella
1216(1)
Infections Due to Other Viruses
1217(3)
Hantavirus Cardiopulmonary Syndrome
1217(1)
Mumps
1218(1)
Rabies
1219(1)
Rickettsial Infections and Q Fever
1220(4)
Human Ehrlichiosis & Anaplasmosis
1221(1)
Rocky Mountain Spotted Fever
1222(1)
Endemic Typhus (Murine Typhus)
1222(1)
Q Fever
1223(1)
41 Human Immunodeficiency Virus Infection
1224(12)
Elizabeth J. McFarland
Pathogenesis & Epidemiology
1224(2)
Prevention
1226(1)
Perinatally HIV-Exposed Infant
1227(1)
Adolescents & Youth with HIV Exposure
1228(1)
Progressive HIV Disease
1229(2)
Treatment
1231(3)
Quality Assurance & Outcome Metrics
1234(2)
42 Infections: Bacterial & Spirochetal
1236(64)
James Gaensbauer
Yosuke Nomura
John W. Ogle
Bacterial Infections
1236(56)
Group A Streptococcal Infections
1236(4)
Group B Streptococcal Infections
1240(3)
Streptococcal Infections with Organisms Other Than Group A or B
1243(1)
Pneumococcal Infections
1244(3)
Staphylococcal Infections
1247(4)
Meningococcal Infections
1251(3)
Gonococcal Infections
1254(2)
Botulism
1256(2)
Tetanus
1258(2)
Gas Gangrene
1260(1)
Diphtheria
1261(2)
Infections Due to Enterobacteriaceae
1263(2)
Pseudomonas Infections
1265(2)
Salmonella Gastroenteritis
1267(2)
Typhoid Fever & Paratyphoid Fever
1269(1)
Shigellosis (Bacillary Dysentery)
1270(1)
Cholera
1271(2)
Campylobacter Infection
1273(1)
Tularemia
1274(1)
Plague
1275(2)
Haemophilus Influenzae Type B Infections
1277(2)
Pertussis (Whooping Cough)
1279(2)
Listeriosis
1281(2)
Tuberculosis
1283(3)
Infections with Nontuberculous Mycobacteria
1286(1)
Legionella Infection
1287(1)
Chlamydophila & Chlamydia Infections (Psittacosis, C Pneumoniae, & C Trachomatis)
1288(2)
Cat-Scratch Disease
1290(2)
Spirochetal Infections
1292(8)
Syphilis
1292(3)
Relapsing Fever
1295(1)
Leptospirosis
1296(2)
Lyme Disease
1298(2)
43 Infections: Parasitic & Mycotic
1300(39)
James Gaensbauer
Myron J. Levin
Parasitic Infections
1300(1)
Protozoal Infections
1301(12)
Systemic Infections
1301(7)
Gastrointestinal Infections
1308(5)
Trichomoniasis
1313(1)
Metazoal Infections
1313(11)
Nematode Infections
1313(7)
Cestode Infections (Flukes)
1320(3)
Trematode Infections
1323(1)
Mycotic Infections
1324(15)
Pneumocystis & Other Opportunistic Fungal Infections
1335(2)
Pneumocystis Jiroveci Infection
1337(2)
44 Sexually Transmitted Infections
1339(22)
Daniel H. Reirden
Ann-Christine Nyquist
Introduction
1339(2)
Adolescent Sexuality
1339(1)
Risk Factors
1340(1)
Prevention of Sexually Transmitted Infections
1340(1)
Screening for Sexually Transmitted Infections
1340(1)
Signs & Symptoms
1341(1)
The Most Common Antibiotic-Responsive Sexually Transmitted Infections
1341(7)
Chlamydia Trachomatis Infection
1341(1)
Neisseria Gonorrhoeae Infection
1342(6)
The Spectrum of Signs & Symptoms of Sexually Transmitted Infections
1348(13)
Cervicitis
1348(1)
Pelvic Inflammatory Disease
1349(1)
Urethritis
1350(1)
Epididymitis
1351(1)
Proctitis, Proctocolitis, & Enteritis
1351(1)
Vaginal Discharge
1351(2)
Genital Ulcerations
1353(3)
Genital Warts & Human Papillomavirus
1356(2)
Other Viral Infections
1358(1)
Ectoparasitic Infections
1359(1)
References
1360(1)
45 Travel Medicine
1361(15)
Suchitra Rao
Introduction
1361(1)
Preparing Children & Infants for Travel
1361(2)
Vaccinations---Routine Childhood Vaccines Modified for Travel
1363(2)
Vaccinations---Travel-Specific
1365(2)
Traveler's Diarrhea
1367(1)
Malaria Prophylaxis & Prevention
1368(1)
Visits to Friends & Relatives (VFR) in High-Risk Areas
1369(1)
HIV & Sexually Transmitted Diseases
1369(3)
Fever in the Returned Traveler
1372(3)
References
1375(1)
46 Chemistry & Hematology Reference Intervals
1376(17)
Melkon G. DomBourian
Aimee LeDoux
Jordana E. Hoppe
Robert Snyder
Challenges in Determining & Interpreting Pediatric Reference Intervals
1376(1)
Guidelines for Use of Data in a Reference Range Study
1376(1)
Statistical Computation of Reference Intervals
1377(1)
Why Reference Intervals Vary
1378(1)
Sensitivity, Specificity, & Predicitive Values
1378(1)
Pediatric Reference Intervals
1379(14)
Index 1393
William W. Hay, Jr., MD Professor, Department of Pediatrics Director, Training Program in Neonatal-Perinatal Medicine Director, Neonatal Clinical Research Center University of Colorado School of Medicine and The Childrens Hospital, Denver





Myron J. Levin, MD Professor, Departments of Pediatrics and Medicine Head, Section of Pediatric Infectious Diseases University of Colorado School of Medicine and The Childrens Hospital, Denver