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CURRENT Diagnosis and Treatment Pediatrics, Twenty-Fourth Edition 24th edition [Minkštas viršelis]

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  • Formatas: Paperback / softback, 1520 pages, aukštis x plotis x storis: 229x185x43 mm, weight: 1896 g, 300 Illustrations
  • Išleidimo metai: 23-May-2018
  • Leidėjas: McGraw-Hill Education
  • ISBN-10: 1259862909
  • ISBN-13: 9781259862908
Kitos knygos pagal šią temą:
  • Formatas: Paperback / softback, 1520 pages, aukštis x plotis x storis: 229x185x43 mm, weight: 1896 g, 300 Illustrations
  • Išleidimo metai: 23-May-2018
  • Leidėjas: McGraw-Hill Education
  • ISBN-10: 1259862909
  • ISBN-13: 9781259862908
Kitos knygos pagal šią temą:
A concise, yet comprehensive source of current information on the medical problems of children –-- from birth through adolescence 

•A practical, up-to-date well-referenced guide to the diagnosis and treatment of the most commonly seen medical conditions in children
•Excellent coverage of The Council on Medical Student Education in Pediatrics (COMSEP) curriculum used in pediatric clerkship
•46 chapters cover a wide range of topics, including neonatal medicine, child development and behavior, emergency and critical care medicine, and diagnosis and treatment of specific disorders according to major problems, etiologies, and organ systems
•A wealth of tables and figures provide quick access to important information, such as acute and critical care procedures in the delivery room, the office, the emergency room, and the critical care unit; anti-infective agents, drug dosages, immunization schedules, differential diagnoses, and developmental disorders
•Includes detailed descriptions of diseases as well as diagnostic and therapeutic procedures
•Complete with handy guide to normal laboratory values 
•Presented in the consistent, easy-to-follow CURRENT format
•Valuable to medical students, pediatric residents, pediatricians, family practitioners, nurses, nurse practitioners, physician assistants, and other healthcare providers who work with infants, children, and adolescents
•Authors are practicing pediatricians to ensure that each chapter reflects the needs and realities of day-to-day practice 

Authors xix
Preface xxix
Selected Highlighted Topics in the 24th Edition of CDT-P xxxi
1 Advancing the Quality & Safety of Care 1(9)
Daniel Hyman
Introduction
1(1)
Current Context
1(3)
Strategies & Models for Quality Improvement (QI)
4(3)
Principles of Patient Safety (Incident Reporting, Just Culture, Disclosure, FMEA, RCA, Reliability, Checklists)
7(3)
2 The Newborn Infant 10(57)
Danielle Smith
Theresa Grover
Introduction
10(1)
The Neonatal History
10(1)
Assessment of Growth & Gestational Age
10(2)
Examination at Birth
12(1)
Examination in the Nursery
13(2)
Care of the Well Neonate
15(3)
Feeding the Well Neonate
15(2)
Early Discharge of the Newborn Infant
17(1)
Hearing Screening
18(1)
Common Problems in the Term Newborn
18(14)
Neonatal Jaundice
18(7)
Hypoglycemia
25(1)
Respiratory Distress in the Term Newborn Infant
26(2)
Heart Murmurs
28(1)
Birth Trauma
28(1)
Infants of Mothers Who Abuse Drugs
29(2)
Multiple Births
31(1)
Neonatal Intensive Care
32(14)
Perinatal Resuscitation
32(4)
The Preterm Infant
36(9)
The Late Preterm Infant
45(1)
Cardiac Problems in the Newborn Infant
46(2)
Structural Heart Disease
46(1)
Persistent Pulmonary Hypertension
47(1)
Arrhythmias
48(1)
Gastrointestinal & Abdominal Surgical Conditions in the Newborn Infant
48(4)
Esophageal Atresia & Tracheoesophageal Fistula
48(1)
Intestinal Obstruction
49(1)
Abdominal Wall Defects
50(1)
Diaphragmatic Hernia
51(1)
Gastrointestinal Bleeding
51(1)
Gastroesophageal Reflux
51(1)
Infections in the Newborn Infant
52(7)
Bacterial Infections
52(3)
Fungal Sepsis
55(1)
Congenital Infections
56(2)
Perinatally Acquired Infections
58(1)
Hematologic Disorders in the Newborn Infant
59(3)
Bleeding Disorders
59(1)
Anemia
60(1)
Polycythemia
61(1)
Renal Disorders in the Newborn Infant
62(1)
Renal Failure
62(1)
Urinary Tract Anomalies
62(1)
Renal Vein Thrombosis
63(1)
Neurologic Problems in the Newborn Infant
63(2)
Seizures
63(1)
Intracranial Hemorrhage
64(1)
Metabolic Disorders in the Newborn Infant
65(1)
Hyperglycemia
65(1)
Hypocalcemia
65(1)
Inborn Errors of Metabolism
66(1)
Quality Assessment & Improvement in the Newborn Nursery & NICU
66(1)
3 Child Development & Behavior 67(31)
Edward Goldson
Ann Reynolds
Introduction
67(1)
Normal Development
67(7)
The First 2 Years
67(6)
Ages 2-4 Years
73(1)
Early School Years: Ages 5-7 Years
74(1)
Middle Childhood: Ages 7-11 Years
74(1)
Behavioral & Developmental Variations
74(1)
Normality & Temperament
74(1)
Enuresis & Encopresis
75(2)
Enuresis
75(1)
Encopresis
76(1)
Common Developmental Concerns
77(8)
Colic
77(2)
Feeding Disorders in Infants & Young Children
79(1)
Sleep Disorders
80(1)
Parasomnias
81(1)
Insomnia
81(1)
Sleep-Disordered Breathing
82(1)
Restless Legs Syndrome & Periodic Limb Movement Disorder
82(1)
Temper Tantrums & Breath-Holding Spells
83(2)
Well-Child Surveillance & Screening
85(12)
Developmental Disorders
85(2)
Attention-Deficit/Hyperactivity Disorder
87(2)
Autism Spectrum Disorders
89(4)
Intellectual Disability
93(2)
Specific Forms of Intellectual Disability & Associated Treatment Issues
95(2)
References
97(1)
4 Adolescence 98(44)
Amy E. Sass
Molly J. Richards
Introduction
98(1)
Epidemiology
98(1)
Mortality Data
98(1)
Morbidity Data
98(1)
Providing a Medical Home for Adolescents
99(1)
Relating to the Adolescent Patient
100(7)
The Structure of the Visit
101(6)
Guidelines for Adolescent Preventive Services
107(7)
Adolescent Screening
107(1)
Promoting Healthy Behaviors
108(4)
Transition to Adult Care
112(2)
Growth & Development
114(3)
Puberty
114(1)
Physical Growth
114(1)
Sexual Maturation
114(1)
Psychosocial Development
115(2)
Adolescent Gynecology & Reproductive Health
117(25)
Breast Examination
117(1)
Breast Masses
118(1)
Nipple Discharge & Galactorrhea
119(1)
Gynecomastia
120(2)
Gynecologic Disorders in Adolescence
122(10)
Contraception
132(7)
Pregnancy
139(3)
5 Adolescent Substance Abuse 142(14)
Paritosh Kaul
Scope of the Problem
142(5)
Morbidity Data
147(1)
Predicting the Progression from use to Abuse
148(1)
Evaluation of Substance Abuse
149(3)
Treatment & Referral
152(2)
Prevention
154(1)
References
155(1)
6 Eating Disorders 156(12)
Eric J. Sigel
Introduction
156(1)
Etiology
156(1)
Incidence
157(1)
Predisposing Factors & Clinical Profiles
157(1)
Anorexia Nervosa
157(6)
Bulimia Nervosa
163(2)
Binge-Eating Disorder
165(1)
Avoidant/Restrictive Food Intake Disorder
166(1)
Prognosis, Quality Assessment, & Outcomes Metrics
166(1)
Resources for Practitioners & Families
167(1)
7 Child & Adolescent Psychiatric Disorders & Psychosocial Aspects of Pediatrics 168(45)
Adam Burstein
Kimberly Kelsay
Ayelet Talmi
Introduction
168(1)
Models of Care Encompassing Behavioral Health in the Primary Care Setting
169(1)
Prevention, Early Identification, & Developmental Context
170(1)
Lifestyle Recommendations
171(1)
Identification & Assessment During Health Supervision Visits
171(9)
Psychiatric Disorders of Childhood & Adolescence
180(9)
Anxiety Disorders
181(8)
Obsessive-Compulsive & Related Disorders
189(24)
Attention-Deficit/Hyperactivity Disorder
192(4)
Mood Disorders
196(6)
Suicide in Children & Adolescents
202(2)
Disruptive, Impulse-Control & Conduct Disorders
204(1)
High-Risk Patients & Homicide
205(2)
Somatic Symptom & Related Disorders
207(2)
Adjustment Disorders
209(1)
Psychotic Disorders
209(3)
Other Psychiatric Conditions
212(1)
8 Child Abuse & Neglect 213(9)
Antonia Chiesa
Andrew P. Sirotnak
Introduction
213(1)
Prevention
214(1)
Clinical Findings
214(6)
Differential Diagnosis
220(1)
Treatment
220(1)
Prognosis
221(1)
9 Ambulatory & Office Pediatrics 222(23)
Meghan Treitz
Daniel Nicklas
Maya Bunik
David Fox
Introduction
222(1)
Pediatric History
222(2)
Pediatric Physical Examination
224(1)
Health Supervision Visits
225(14)
Developmental & Behavioral Assessment
225(3)
Growth Parameters
228(1)
Blood Pressure
229(1)
Vision & Hearing Screening
230(4)
Anticipatory Guidance
234(1)
Nutrition Counseling
235(1)
Counseling About Television & Other Media
236(1)
Immunizations
237(1)
Acute-Care Visits
237(1)
Prenatal Visits
238(1)
Sports Physicals
238(1)
Chronic Disease Management
238(1)
Medical Home
239(1)
Mental & Behavioral Health
239(1)
Telephone Management & Web-Based Information
240(1)
Advocacy & Community Pediatrics
240(1)
Common General Pediatric Issues
241(5)
Fever
241(2)
Growth Deficiency
243(2)
10 Immunization 245(35)
Matthew F. Daley
Sean T. O'Leary
Ann-Christine Nyquist
Standards for Pediatric Immunization Practices
246(1)
Routine Childhood & Adolescent Immunization Schedules
247(27)
Vaccine Safety
247(7)
Vaccination in Special Circumstances
254(1)
Hepatitis B Vaccination
255(3)
Rotavirus Vaccination
258(1)
Diphtheria-Tetanus-Acellular Pertussis Vaccination
259(2)
Haemophilus Influenzae Type B Vaccination
261(1)
Pneumococcal Vaccination
262(2)
Poliomyelitis Vaccination
264(1)
Influenza Vaccination
265(1)
Measles, Mumps, & Rubella Vaccination
266(2)
Varicella Vaccination
268(2)
Hepatitis A Vaccination
270(1)
Meningococcal Vaccination
271(2)
Tetanus-Reduced Diphtheria-Acellular Pertussis Vaccination (Adolescents & Adults)
273(1)
Human Papillomavirus Vaccination
273(1)
Vaccinations for Special Situations
274(6)
Rabies Vaccination
274(2)
Typhoid Fever Vaccination
276(1)
Cholera Vaccination
277(1)
Japanese Encephalitis Vaccination
277(1)
Tuberculosis Vaccination
277(1)
Yellow Fever Vaccination
278(1)
Passive Prophylaxis
278(2)
11 Normal Childhood Nutrition & Its Disorders 280(29)
Matthew A. Haemer
Laura E. Primak
Nancy F. Krebs
Nutritional Requirements
280(8)
Nutrition & Growth
280(1)
Energy
280(1)
Protein
281(1)
Lipids
282(1)
Carbohydrates
283(1)
Major Minerals
284(1)
Trace Elements
284(1)
Vitamins
284(4)
Infant Feeding
288(8)
Breast-Feeding
288(7)
Special Dietary Products for Infants
295(1)
Nutrition for Children 2 Years & Older
296(6)
Pediatric Undernutrition
297(1)
Pediatric Overweight & Obesity
298(4)
Nutrition Support
302(7)
Enteral
302(1)
Parenteral Nutrition
303(1)
Nutrient Requirements & Delivery
304(5)
12 Emergencies & Injuries 309(23)
Kevin R. Carney
Kelley Roswell
Introduction to Pediatric Emergencies & Injuries
309(7)
Initial Approach to the Acutely Ill Infant or Child
309(1)
The ABCs of Resuscitation
310(4)
Management of Shock
314(1)
Summary of Initial Approach to the Acutely Ill Infant or Child
315(1)
Emergency Pediatric Drugs
316(1)
Approach to the Pediatric Trauma Patient
316(5)
Mechanism of Injury
317(1)
Initial Assessment & Management
317(1)
Primary Survey
317(2)
Secondary Survey
319(2)
Head Injury
321(2)
Burns
323(3)
Thermal Burns
323(2)
Electrical Burns
325(1)
Disorders due to Extremes of Environment
326(1)
Heat-Related Illnesses & Heat Stroke
326(1)
Hypothermia
326(1)
Submersion Injuries
327(1)
Lacerations
328(1)
Animal & Human Bites
329(1)
Dog Bites
329(1)
Cat Bites
330(1)
Human Bites
330(1)
Pain Management & Procedural Sedation
330(2)
13 Poisoning 332(30)
Richard C. Dart
Barry H. Rumack
George Sam Wang
Introduction
332(1)
Pharmacologic Principles of Toxicology
332(1)
Preventing Childhood Poisonings
333(1)
General Treatment of Poisoning
333(4)
Initial Telephone Contact
333(3)
Initial Emergency Department Contact
336(1)
Definitive Therapy of Poisoning
336(1)
Management of Specific Common Poisonings
337(25)
Acetaminophen (Paracetamol)
337(2)
Alcohol, Ethyl (Ethanol)
339(1)
Amphetamines & Related Drugs (Stimulants, Methamphetamine, MDMA)
340(1)
Anesthetics, Local
340(1)
Antihistamines & Cough & Cold Preparations
341(1)
Barbiturates & Benzodiazepines
342(1)
Belladonna Alkaloids (Atropine, Jimsonweed, Potato Leaves, Scopolamine, Stramonium)
342(1)
β-Blockers & Calcium Channel Blockers
343(1)
Carbon Monoxide
343(1)
Caustics
344(1)
Central α2-Adrenergic Agonist
344(1)
Cocaine
345(1)
Cosmetics & Related Products
345(1)
Cyclic Antidepressants
345(1)
Digitalis & Other Cardiac Glycosides
346(1)
Diphenoxylate with Atropine (Lomotil) & Loperamide (Imodium)
346(1)
Disinfectants & Deodorizers
347(1)
Disk-Shaped "Button" Batteries
347(1)
Ethylene Glycol & Methanol
348(1)
γ-Hydroxybutyrate, γ-Butyrolactone, Butanediol, Flunitrazepam, & Ketamine
348(1)
Hydrocarbons (Benzene, Charcoal Lighter Fluid, Gasoline, Kerosene, Petroleum Distillates, Turpentine)
349(1)
Ibuprofen
349(1)
Insect Stings (Bee, Wasp, & Hornet)
349(1)
Insecticides
349(1)
Iron
350(1)
Lead
351(1)
Magnets
352(1)
Marijuana
352(1)
Mushrooms
352(1)
Nitrites, Nitrates, Aniline, Pentachlorophenol, & Dinitrophenol
353(1)
Opioids & Opiates
353(1)
Oral Anti-Diabetics (Sulfonylureas, Metformin)
354(1)
Antipsychotics (Typical & Atypical)
355(1)
Plants
355(1)
Psychotropic Drugs
355(2)
Salicylates
357(1)
Scorpion Stings
358(1)
Serotonin Reuptake Inhibitors
358(1)
Snakebite
358(1)
Soaps & Detergents
359(1)
Spider Bites
360(1)
Vitamins
360(1)
Warfarin (Coumadin) & Newer Oral Anticoagulants (NOAC)
361(1)
14 Critical Care 362(37)
Todd C. Carpenter
Amy Clevenger
Angela S. Czaja
Eva N. Grayck
Cameron F. Gunville
Leslie Ridal
Carleen Zebuhr
Introduction
362(1)
Respiratory Critical Care
362(8)
Acute Respiratory Failure
362(4)
Conventional Mechanical Ventilation
366(3)
Other Modes of Respiratory Support
369(1)
Major Respiratory Diseases in the Pediatric ICU
370(6)
Acute Respiratory Distress Syndrome
370(3)
Status Asthmaticus
373(3)
Cardiovascular Critical Care
376(7)
Shock
376(3)
Sepsis
379(4)
Neurocritical Care
383(5)
Traumatic Brain Injury
383(4)
Hypoxic-Ischemic Encephalopathy
387(1)
Acute Kidney Injury & Renal Replacement Therapy
388(1)
Fluid Management & Nutritional Support of the Critically Ill Child
389(2)
Sedation & Analgesia in the Pediatric ICU
391(4)
End-of-Life Care & Death in the PICU
395(3)
Quality Improvement Initiatives in the PICU
398(1)
15 Skin 399(21)
Lori D. Prok
Carla X. Torres-Zegarra
General Principles
399(2)
Diagnosis of Skin Disorders
399(1)
Treatment of Skin Disorders
399(2)
Disorders of the Skin in Newborns
401(5)
Transient Diseases in Newborns
401(1)
Pigment Cell Birthmarks, Nevi, & Melanoma
402(1)
Melanocytic Nevi
402(1)
Vascular Birthmarks
403(1)
Epidermal Birthmarks
404(1)
Connective Tissue Birthmarks (Juvenile Elastoma, Collagenoma)
404(1)
Hereditary Skin Disorders
405(1)
Common Skin Diseases in Infants, Children, & Adolescents
406(14)
Acne
406(2)
Bacterial Infections of the Skin
408(1)
Fungal Infections of the Skin
409(1)
Viral Infections of the Skin
410(1)
Virus-Induced Tumors
411(1)
Insect Infestations
412(1)
Dermatitis (Eczema)
412(3)
Common Skin Tumors
415(1)
Papulosquamous Eruptions
416(1)
Hair Loss (Alopecia)
417(1)
Reactive Erythemas
418(1)
Miscellaneous Skin Disorders Seen in Pediatric Practice
418(2)
16 Eye 420(46)
Jennifer Lee Jung
Rebecca Sands Braverman
Introduction
420(1)
Common Nonspecific Signs & Symptoms
420(1)
Red Eye
420(1)
Tearing
420(1)
Discharge
420(1)
Pain & Foreign Body Sensation
420(1)
Photophobia
420(1)
Leukocoria
421(1)
Refractive Errors
421(1)
Myopia (Nearsightedness)
422(1)
Hyperopia (Farsightedness)
422(1)
Astigmatism
422(1)
Ophthalmic Examination
422(4)
History
422(1)
Visual Acuity
422(1)
External Examination
423(1)
Pupils
424(1)
Alignment & Motility Evaluation
424(1)
Ophthalmoscopic Examination
425(1)
Ocular Trauma
426(7)
Ocular Foreign Bodies
426(1)
Corneal Abrasion
427(1)
Intraocular Foreign Bodies & Perforating Ocular Injuries
428(1)
Blunt Orbital Trauma
429(1)
Lacerations
429(1)
Burns
430(1)
Hyphema
431(1)
Abusive Head Trauma & Nonaccidental Trauma
432(1)
Prevention of Ocular Injuries
432(1)
Disorders of the Ocular Structures
433(4)
Diseases of the Eyelids
433(1)
Viral Eyelid Disease
434(1)
Miscellaneous Eyelid Infections
435(1)
Eyelid Ptosis
435(1)
Homer Syndrome
436(1)
Eyelid Tics
437(1)
Disorders of the Nasolacrimal System
437(2)
Nasolacrimal Duct Obstruction
437(1)
Congenital Dacryocystocele
438(1)
Dacryocystitis
438(1)
Diseases of the Conjunctiva
439(4)
Ophthalmia Neonatorum
439(1)
Bacterial Conjunctivitis
440(1)
Viral Conjunctivitis
440(1)
Allergic Conjunctivitis
441(1)
Mucocutaneous Diseases
442(1)
Disorders of the Iris
443(2)
Iris Coloboma
443(1)
Aniridia
444(1)
Albinism
444(1)
Miscellaneous Iris Conditions
445(1)
Glaucoma
445(1)
Uveitis
445(3)
Anterior Uveitis/Iridocyclitis/Iritis
446(1)
Posterior Uveitis
446(1)
Intermediate Uveitis
447(1)
Disorders of the Cornea
448(2)
Cloudy Cornea
448(1)
Viral Keratitis
448(1)
Corneal Ulcers
449(1)
Disorders of the Lens
450(1)
Cataracts
450(1)
Dislocated Lenses/Ectopia Lentis
450(1)
Disorders of the Retina
451(3)
Retinal Hemorrhages in the Newborn
451(1)
Retinopathy of Prematurity
451(1)
Retinoblastoma
452(1)
Retinal Detachment
453(1)
Diabetic Retinopathy
454(1)
Diseases of the Optic Nerve
454(4)
Optic Neuropathy
454(1)
Optic Nerve Hypoplasia
455(1)
Papilledema
456(1)
Optic Neuritis
457(1)
Optic Atrophy
458(1)
Diseases of the Orbit
458(8)
Periorbital & Orbital Cellulitis
458(1)
Craniofacial Anomalies
459(1)
Orbital Tumors
459(1)
Nystagmus
460(1)
Amblyopia
461(1)
Strabismus
462(2)
Unexplained Decreased Vision in Infants & Children
464(1)
Learning Disabilities & Dyslexia
464(2)
17 Oral Medicine & Dentistry 466(12)
Ulrich Klein
Roopa P. Gandhi
Camille V. Gannam
Issues in Pediatric Oral Health
466(1)
Oral Examination of Children
467(2)
Eruption of the Teeth
469(2)
Dental Caries
471(2)
Periodontal Disease
473(1)
Dental Emergencies
474(1)
Special Patient Populations
475(2)
Orthodontic Referral
477(1)
18 Ear, Nose, & Throat 478(31)
Patricia J. Yoon
Melissa A. Scholes
Norman R. Friedman
The Ear
478(14)
Infections of the Ear
478(10)
Acute Trauma to the Middle Ear
488(1)
Ear Canal Foreign Body & Cerumen Impaction
488(1)
Auricular Hematoma
489(1)
Congenital Ear Malformations
489(1)
Identification & Management of Hearing Loss
489(3)
The Nose & Paranasal Sinuses
492(5)
Acute Viral Rhinitis
492(1)
Rhinosinusitis
493(2)
Choanal Atresia
495(1)
Recurrent Rhinitis
495(1)
Epistaxis
496(1)
Nasal Infection
497(1)
Nasal Trauma
497(1)
Foreign Bodies in the Nose
497(1)
The Throat & Oral Cavity
497(12)
Acute Stomatitis
497(1)
Pharyngitis
498(3)
Peritonsillar Cellulitis or Abscess (Quinsy)
501(1)
Retropharyngeal Abscess
501(1)
Ludwig Angina
501(1)
Acute Cervical Adenitis
502(1)
Snoring, Mouth Breathing, & Upper Airway Obstruction
503(2)
Tonsillectomy & Adenoidectomy
505(1)
Disorders of the Lips
506(1)
Disorders of the Tongue
506(1)
Halitosis
506(1)
Salivary Gland Disorders
507(1)
Congenital Oral Malformations
507(2)
19 Respiratory Tract & Mediastinum 509(52)
Monica J. Federico
Christopher D. Baker
Emily M. Deboer
Ann C. Halbower
Oren Kupfer
Stacey L. Martiniano
Scott D. Sagel
Paul Stillwell
Edith T. Zemanick
Michelle Caraballo
Stephen Hawkins
Respiratory Tract
509(1)
Growth & Development
509(1)
Diagnostic Aids
510(5)
Physical Examination of the Respiratory Tract
510(1)
Pulmonary Function Tests
510(1)
Assessment of Oxygenation & Ventilation
511(1)
Diagnosis of Respiratory Tract Infections
512(2)
Imaging of the Respiratory Tract
514(1)
Laryngoscopy & Bronchoscopy
515(1)
General Therapy for Pediatric Lung Diseases
515(2)
Oxygen Therapy
515(1)
Inhalation of Medications
516(1)
Airway Clearance Therapy
516(1)
Avoidance of Evironmental Hazards
517(1)
Disorders of the Conducting Airways
517(1)
Laryngomalacia & Congenital Disorders of the Extrathoracic Airway
518(1)
Laryngomalacia
518(1)
Other Causes of Congenital Extrathoracic Obstruction
518(1)
Acquired Disorders of the Extrathoracic Airway
519(4)
Foreign Body Aspiration in the Extrathoracic Airway
519(1)
Croup Syndromes
520(2)
Vocal Fold Immobility
522(1)
Subglottic Stenosis
522(1)
Congenital Causes of Intrathoracic Airway Obstruction
523(2)
Malacia of Airways
523(1)
Vascular Rings & Slings
524(1)
Bronchogenic Cysts
524(1)
Acquired Causes of Intrathoracic Airway Obstruction
525(1)
Foreign Body Aspiration in the Intrathoracic Airway
525(1)
Disorders of Mucociliary Clearance
525(4)
Cystic Fibrosis
526(1)
Primary Ciliary Dyskinesia
527(1)
Bronchiectasis
528(1)
Congenital Malformations of the Lung Parenchyma
529(4)
Pulmonary Agenesis & Hypoplasia
529(1)
Pulmonary Sequestration
530(1)
Congenital Lobar Overinflation
531(1)
Congenital Pulmonary Airway Malformation (Cystic Adenomatoid Malformation)
532(1)
Acquired Abnormalities of the Lung Parenchyma
533(4)
Bronchopulmonary Dysplasia
533(1)
Community-Acquired Bacterial Pneumonia
534(2)
Parapneumonic Effusion & Empyema
536(1)
Atypical Pneumonias
537(6)
Viral Pneumonia
537(1)
Bronchiolitis
538(1)
Mycoplasma Pneumonia
539(1)
Aspiration Pneumonia
540(1)
Pneumonia in the Immunocompromised Host
541(1)
Lung Abscess
542(1)
Bronchiolitis Obliterans
543(3)
Children's Interstitial Lung Disease Syndrome
544(1)
Hypersensitivity Pneumonitis
545(1)
Diseases of the Pulmonary Circulation
546(4)
Pulmonary Hemorrhage
546(2)
Pulmonary Embolism
548(1)
Pulmonary Edema
549(1)
Congenital Pulmonary Lymphangiectasia
549(1)
Disorders of the Chest Wall
550(1)
Scoliosis
550(1)
Pectus Carinatum
550(1)
Pectus Excavatum
550(1)
Neuromuscular Disorders & Lung Disease
551(1)
Disorders of the Pleura & Pleural Cavity
551(2)
Hemothorax
552(1)
Chylothorax
552(1)
Pneumothorax & Related Air Leak Syndromes
552(1)
Mediastinum
553(1)
Mediastinal Masses
553(1)
Sleep-Disordered Breathing
554(1)
Obstructive & Central Sleep Apnea
554(1)
Apparent Life-Threatening Events
555(6)
Sudden Unexpected Infant Death & Sudden Infant Death Syndrome
558(1)
Quality Assessment & Outcomes Metrics
559(2)
20 Cardiovascular Diseases 561(65)
Pei-Ni Jone
Johannes Von Alvensleben
Dale Burkett
Jeffrey R. Darst
Kathryn K. Collins
Shelley D. Miyamoto
Introduction
561(1)
Diagnostic Evaluation
561(9)
History
561(1)
Physical Examination
561(3)
Electrocardiography
564(2)
Chest Radiograph
566(1)
Echocardiography
567(1)
Magnetic Resonance Imaging
568(1)
Cardiopulmonary Stress Testing
568(1)
Arterial Blood Gases
568(1)
Cardiac Catheterization & Angiocardiography
569(1)
Perinatal & Neonatal Circulation
570(1)
Heart Failure
571(2)
Genetic Basis of Congenital Heart Disease
573(1)
Acyanotic Congenital Heart Disease
574(14)
Defects in Septation
574(4)
Patent (Persistent) Ductus Arteriosus
578(2)
Right-Sided Obstructive Lesions
580(2)
Left-Sided Lesions
582(4)
Diseases of the Aorta
586(1)
Coronary Artery Abnormalities
587(1)
Cyanotic Congenital Heart Disease
588(10)
Tetralogy of Fallot
588(2)
Pulmonary Atresia with Ventricular Septal Defect
590(1)
Pulmonary Atresia with Intact Ventricular Septum
590(2)
Tricuspid Atresia
592(1)
Hypoplastic Left Heart Syndrome
593(1)
Transposition of the Great Arteries
594(2)
Total Anomalous Pulmonary Venous Return
596(1)
Truncus Arteriosus
597(1)
Quality Improvement in Congenital Heart Disease
598(1)
Acquired Heart Disease
599(10)
Rheumatic Fever
599(2)
Kawasaki Disease
601(1)
Infective Endocarditis
602(2)
Pericarditis
604(1)
Cardiomyopathy
605(3)
Myocarditis
608(1)
Preventive Cardiology
609(1)
Hypertension
609(1)
Atherosclerosis & Dyslipidemias
609(1)
Chest Pain
610(1)
Cardiac Transplantation
611(1)
Quality Improvement for Pediatric Heart Transplantation
612(1)
Pulmonary Hypertension
613(1)
Disorders of Rate & Rhythm
614(9)
Disorders of the Sinus Node
614(1)
Premature Beats
615(1)
Supraventricular Tachycardia
616(4)
Ventricular Tachycardia
620(1)
Long QT Syndrome
621(1)
Sudden Death
621(1)
Disorders of Atrioventricular Conduction
621(2)
Syncope (Fainting)
623(3)
Introduction
623(1)
Diagnostic Evaluation
624(1)
Vasovagal/Neurocardiogenic Syncope
624(2)
21 Gastrointestinal Tract 626(43)
Edward J. Hoffenberg
Glenn T. Furuta
Gregory Kobak
Thomas Walker
Jason Soden
Robert E. Kramer
David Brumbaugh
Disorders of the Esophagus
626(7)
Gastroesophageal Reflux & GERD
626(2)
Eosinophilic Esophagitis
628(1)
Achalasia of the Esophagus
629(1)
Caustic Burns of the Esophagus
630(1)
Foreign Bodies in the Alimentary Tract
631(2)
Disorders of the Stomach & Duodenum
633(4)
Hiatal Hernia
633(1)
Pyloric Stenosis
633(1)
Gastric & Duodenal Ulcer
634(1)
Congenital Diaphragmatic Hernia
635(1)
Congenital Duodenal Obstruction
636(1)
Disorders of the Small Intestine
637(6)
Intestinal Atresia & Stenosis
637(1)
Intestinal Malrotation
638(1)
Short Bowel Syndrome
638(2)
Intussusception
640(1)
Inguinal Hernia
640(1)
Umbilical Hernia
641(1)
Patent Omphalomesenteric Duct
641(1)
Meckel Diverticulum
641(1)
Acute Appendicitis
642(1)
Duplications of the Gastrointestinal Tract
643(1)
Disorders of the Colon
643(5)
Congenital Aganglionic Megacolon (Hirschsprung Disease)
643(1)
Constipation
644(2)
Anal Fissure
646(1)
Congenital Anorectal Anomalies
646(1)
Clostridium Difficile Infection in Children
647(1)
Disorders of the Peritoneal Cavity
648(4)
Peritonitis
648(1)
Chylous Ascites
648(1)
Gastrointestinal Tumors & Malignancies
649(1)
Juvenile Polyps
649(2)
Cancers of the Esophagus, Small Bowel, & Colon
651(1)
Mesenteric Cysts
651(1)
Intestinal Hemangiomas & Vascular Malformations
651(1)
Major Gastrointestinal Symptoms & Signs
652(17)
Acute Diarrhea
652(1)
Chronic Diarrhea
653(2)
Gastrointestinal Bleeding
655(3)
Vomiting
658(2)
Abdominal Pain
660(1)
Acute Abdomen
661(1)
Malabsorption Syndromes
661(4)
Inflammatory Bowel Disease
665(4)
22 Liver & Pancreas 669(47)
Ronald J. Sokol
Michael R. Narkewicz
Shikha S. Sundaram
Cara L. Mac
Liver Disorders
669(39)
Neonatal Cholestatic Jaundice
669(1)
Intrahepatic Cholestasis
669(9)
Extrahepatic Neonatal Cholestasis
678(2)
Other Neonatal Hyperbilirubinemic Conditions (Noncholestatic Nonhemolytic)
680(3)
Hepatitis A
683(2)
Hepatitis B
685(2)
Hepatitis C
687(1)
Hepatitis D (Delta Agent)
688(1)
Hepatitis E
688(1)
Other Hepatitis Viruses
688(1)
Acute Liver Failure
689(1)
Autoimmune Hepatitis
690(2)
Nonalcoholic Fatty Liver Disease
692(1)
α1-Antitrypsin Deficiency Liver Disease
693(1)
Wilson Disease (Hepatolenticular Degeneration)
694(2)
Drug-Induced Liver Disease
696(1)
Cirrhosis
696(2)
Portal Hypertension
698(3)
Biliary Tract Disease
701(4)
Pyogenic & Amebic Liver Abscess
705(1)
Liver Tumors
706(2)
Liver Transplantation
708(1)
Pancreatic Disorders
708(7)
Acute Pancreatitis
708(2)
Chronic Pancreatitis
710(1)
Gastrointestinal & Hepatobiliary Manifestations of Cystic Fibrosis
711(1)
Syndromes with Pancreatic Exocrine Insufficiency
711(3)
Isolated Exocrine Pancreatic Enzyme Defect
714(1)
Pancreatic Tumors
714(1)
References
715(1)
23 Fluid, Electrolyte, & Acid-Base Disorders & Therapy 716(10)
Melisha G. Hanna
Margret Bock
Regulation of Body Fluids, Electrolytes, & Tonicity
716(1)
Acid-Base Balance
717(1)
Fluid & Electrolyte Management
717(7)
Dehydration
719(2)
Hyponatremia
721(1)
Hypernatremia
722(1)
Potassium Disorders
722(2)
Acid-Base Disturbances
724(2)
Metabolic Acidosis
724(1)
Metabolic Alkalosis
725(1)
Respiratory Acidosis
725(1)
Respiratory Alkalosis
725(1)
24 Kidney & Urinary Tract 726(26)
Melissa A. Cadnapaphornchai
Gary M. Lum
Evaluation of the Kidney & Urinary Tract
726(4)
History
726(1)
Physical Examination
726(1)
Laboratory Evaluation of Renal Function
726(4)
Laboratory Evaluation of Immunologic Function
730(1)
Radiographic Evaluation
730(1)
Renal Biopsy
730(1)
Congenital Anomalies of the Urinary Tract
730(2)
Renal Parenchymal Anomalies
730(1)
Distal Urinary Tract Anomalies
731(1)
Hematuria & Glomerular Disease
732(2)
Microhematuria
732(1)
Glomerulonephritis
732(2)
Tubulointerstitial Disease
734(1)
Acute Interstitial Nephritis
734(1)
Proteinuria & Renal Disease
734(1)
Congenital Nephrosis (Finnish Type)
735(1)
Idiopathic Nephrotic Syndrome of Childhood
735(1)
Focal Segmental Glomerulosclerosis
736(1)
Membranous Nephropathy (Membranous Glomerulonephritis)
736(1)
Diseases of the Renal Vessels
736(2)
Renal Vein Thrombosis
736(1)
Renal Arterial Disease
737(1)
Hemolytic-Uremic Syndrome
737(1)
Renal Failure
738(4)
Acute Kidney Injury
738(3)
Chronic Renal Failure
741(1)
Hypertension
742(3)
Inherited or Developmental Defects of the Kidneys
745(4)
Disorders of the Renal Tubules
746(1)
Cystinosis
746(1)
Oculocerebrorenal Syndrome (Lowe Syndrome)
747(1)
Hypokalemic Alkalosis (Bartter Syndrome, Gitelman Syndrome, & Liddle Syndrome)
747(1)
Nephrogenic Diabetes Insipidus (NDI)
747(1)
Nephrolithiasis
748(1)
Urinary Tract Infections
749(1)
QA/QI in Pediatric Nephrology
750(2)
25 Neurologic & Muscular Disorders 752(72)
Teri L. Schreiner
Michele L. Yang
Jan A. Martin
Ricka Messer
Scott Demarest
Diana Walleigh
Neurologic Assessment & Neurodiagnostics
752(6)
History & Examination
752(1)
Diagnostic Testing
752(2)
Pediatric Neuroradiologic Procedures
754(4)
Disorders Affecting the Nervous System in Infants & Children
758(36)
Altered States of Consciousness (Coma)
758(3)
Seizures & Epilepsy
761(12)
Sleep Disorders
773(1)
Headaches
774(3)
Pseudotumor Cerebri (Idiopathic Intracranial Hypertension)
777(2)
Cerebrovascular Disease
779(3)
Congenital Malformations of the Nervous System
782(3)
Abnormal Head Size
785(2)
Neurocutaneous Dysplasias
787(7)
Central Nervous System Degenerative Disorders of Infancy & Childhood
794(1)
Ataxias of Childhood
794(7)
Acute Ataxias of Childhood
794(3)
Chronic & Episodic Ataxias
797(1)
Movement Disorders
797(3)
Cerebral Palsy
800(1)
Infections & Inflammatory Disorders of the Central Nervous System
801(6)
Bacterial Meningitis
802(1)
Brain Abscess
803(1)
Viral Infections
804(1)
Encephalopathy of Human Immunodeficiency Virus Infection
804(1)
Other Infections
805(1)
Noninfectious Inflammatory Disorders of the Central Nervous System
805(1)
Multiple Sclerosis
806(1)
Syndromes Presenting as Acute Flaccid Weakness
807(14)
Disorders of Childhood Affecting Muscles
810(7)
Benign Acute Childhood Myositis
817(1)
Myasthenic Syndromes
817(2)
Peripheral Nerve Palsies
819(1)
Chronic Polyneuropathy
820(1)
Miscellaneous Neuromuscular Disorders
821(3)
Floppy Infant Syndrome
821(3)
26 Orthopedics 824(26)
Jason Rhodes
Mark A. Erickson
Alex Tagawa
Cameron Niswander
Disturbances of Prenatal Origin
824(1)
Congenital Amputations & Limb Deficiencies
824(1)
Deformities of the Extremities
825(6)
Common Foot Problems
825(2)
Genu Varum & Genu Valgum
827(1)
Tibial Torsion & Femoral Anteversion
828(1)
Developmental Dysplasia of the Hip Joint
828(2)
Slipped Capital Femoral Epiphysis
830(1)
Common Spine Conditions
831(2)
Torticollis
831(1)
Scoliosis
832(1)
Kyphosis
832(1)
Inflammatory Conditions
833(1)
Arthritis & Tenosynovitis
833(1)
Syndromes with Musculoskeletal Involvement
834(2)
Arthrogryposis Multiplex Congenita (Amyoplasia Congenita)
834(1)
Klippel-Feil Syndrome
834(2)
Neurologic Disorders Involving the Musculoskeletal System
836(1)
Trauma
837(3)
Traumatic Subluxations & Dislocations
839(1)
Fractures
840(2)
Infections of the Bones & Joints
842(3)
Vascular Lesions & Avascular Necrosis (Osteochondroses)
845(1)
Neoplasia of the Musculoskeletal System
846(2)
Miscellaneous Diseases of Bone & Joint
848(1)
Fibrous Dysplasia
848(1)
Bone Cysts, Baker Cyst, & Ganglions
849(1)
Quality Assurance/Improvement Initiatives in Orthopedics
849(1)
27 Sports Medicine 850(30)
Katherine S. Dahab
Kyle B. Nagle
Armando Vidal
Basic Principles
850(10)
Fitness & Conditioning
850(1)
Sports Nutrition
851(1)
Preparticipation Physical Evaluation
851(8)
Rehabilitation of Sports Injuries
859(1)
Common Sports Medicine Issues & Injuries
860(18)
Infectious Diseases
860(1)
Head & Neck Injuries
860(4)
Spine Injuries
864(1)
Shoulder Injuries
865(2)
Elbow Injurits
867(2)
Hand & Wrist injuries
869(2)
Hip Injuries
871(2)
Knee Injuries
873(4)
Foot & Ankle Injuries
877(1)
Prevention
878(2)
28 Rehabilitation Medicine 880(9)
Gerald H. Clayton
Pamela E. Wilson
Pediatric Brain Injury
880(3)
Spinal Cord Injury
883(2)
Brachial Plexus Lesions & Typical Features
885(1)
Common Rehabilitation Problems
886(2)
Quality Assurance/Improvement Initiatives in Rehabilitation Medicine
888(1)
29 Rheumatic Diseases 889(9)
Jennifer B. Soep
Juvenile Idiopathic Arthritis
889(3)
Systemic Lupus Erythematosus
892(2)
Dermatomyositis
894(1)
Vasculitis
895(1)
Raynaud Phenomenon
896(1)
Noninflammatory Pain Syndromes
896(2)
30 Hematologic Disorders 898(55)
Daniel R. Ambruso
Rochelle Nuss
Michael Wang
Normal Hematologic Values
898(1)
Bone Marrow Failure
898(1)
Constitutional Aplastic Anemia (Fanconi Anemia)
898(2)
Acquired Aplastic Anemia
900(1)
Anemias
901(18)
Approach to the Child with Anemia
901(2)
Pure Red Cell Aplasia
903(1)
Nutritional Anemias
904(2)
Anemia of Chronic Disorders
906(1)
Congenital Hemolytic Anemias: Red Cell Membrane Defects
907(2)
Congenital Hemolytic Anemias: Hemoglobinopathies
909(7)
Congenital Hemolytic Anemias: Disorders of Red Cell Metabolism
916(1)
Acquired Hemolytic Anemia
917(2)
Polycythemia & Methemoglobinemia
919(1)
Methemoglobinemia
920(1)
Disorders of Leukocytes
920(23)
Neutropenia
920(2)
Neutrophilia
922(1)
Disorders of Neutrophil Function
923(2)
Lymphocytosis
925(1)
Eosinophilia
925(1)
Bleeding Disorders
925(2)
Abnormalities of Platelet Number or Function
927(4)
Inherited Bleeding Disorders
931(4)
Von Willebrand Disease
935(1)
Acquired Bleeding Disorders
936(2)
Vascular Abnormalities Associated with Bleeding
938(1)
Thrombotic Disorders
939(4)
Splenic Abnormalities
943(1)
Splenomegaly & Hypersplenism
943(1)
Asplenia & Splenectomy
943(1)
Transfusion Medicine
944(9)
Donor Screening & Blood Processing: Risk Management
944(1)
Storage & Preservation of Blood & Blood Components
944(1)
Pretransfusion Testing
945(4)
Transfusion Practice
949(3)
References
952(1)
31 Neoplastic Disease 953(33)
John A. Craddock
Ralph R. Quinones
Amy K. Keating
Kelly Maloney
Jean M. Mulcahy Levy
Roger H. Giller
Brian S. Greffe
Anna Franklin
Timothy Garrington
Major Pediatric Neoplastic Diseases
953(28)
Acute Lymphoblastic Leukemia
953(4)
Acute Myeloid Leukemia
957(2)
Myeloproliferative Diseases
959(2)
Brain Tumors
961(4)
Lymphomas & Lymphoproliferative Disorders
965(5)
Neuroblastoma
970(2)
Wilms Tumor (Nephroblastoma)
972(2)
Bone Tumors
974(2)
Rhabdomyosarcoma
976(1)
Retinoblastoma
977(1)
Hepatic Tumors
978(2)
Langerhans Cell Histiocytosis
980(1)
Hematopoietic Stem Cell Transplant
981(2)
General Considerations
981(2)
Late Effects of Pediatric Cancer Therapy
983(3)
Growth Complications
983(1)
Endocrine Complications
983(1)
Cardiopulmonary Complications
984(1)
Renal Complications
984(1)
Neuropsychological Complications
984(1)
Second Malignancies
985(1)
32 Pain Management & Pediatric Palliative & End-of-Life Care 986(11)
Brian S. Greffe
Jeffrey L. Galinkin
Nancy A. King
Introduction
986(1)
Pain Assessment
986(1)
Acute Pain
986(3)
Chronic Pain Management
989(2)
Pediatric Palliative & End-of-Life Care
991(1)
Introduction
991(1)
Children Who May Benefit from Palliative Care Interventions
991(1)
Pain Management in Pediatric Palliative Care
992(1)
Quality-of-Life Adjuncts & Symptom Management in Pediatric Palliative Care
992(1)
Psychosocial Aspects of Pediatric Palliative Care
992(1)
Children's Concept of Death
992(1)
Spiritual & Cultural Support
993(1)
Withdrawal of Medical Life Support
994(1)
Advance Care Planning
994(2)
References
996(1)
33 Immunodeficiency 997(19)
Jordan K. Abbott
Pia J. Hauk
Immunodeficiency Evaluation: Primary Considerations
997(4)
Severe Combined Immunodeficiency Diseases
1001(1)
SCID Classification
1002(2)
Other Combined Immunodeficiencies
1004(2)
Antibody Deficiency Syndromes
1006(4)
Phagocyte Disorders
1010(1)
Deficiencies of the Innate Immune System
1011(2)
Immunodeficiency Diseases That Present with Autoimmunity
1013(1)
Immunodeficiency Diseases That Overlap with Allergy
1014(2)
34 Endocrine Disorders 1016(38)
Sarah Bartz
Jennifer M. Barker
Michael S. Kappy
Megan Moriarty Kelsey
Sharon H. Travers
Philip S. Zeitler
General Concepts
1016(1)
Hormone Types
1016(1)
Feedback Control of Hormone Secretion
1016(1)
Disturbances of Growth
1017(8)
Target Height & Skeletal Maturation
1018(1)
Short Stature
1018(6)
Tall Stature
1024(1)
Disorders of the Posterior Pituitary Gland
1025(1)
Arginine Vasopressin (Antidiuretic Hormone) Physiology
1025(1)
Central Diabetes Insipidus
1025(1)
Thyroid Gland
1026(5)
Fetal Development of the Thyroid
1026(1)
Physiology
1026(1)
Hypothyroidism (Congenital & Acquired)
1027(1)
Thyroiditis
1028(1)
Hyperthyroidism
1029(2)
Thyroid Cancer
1031(1)
Disorders of Calcium & Phosphorus Metabolism
1031(6)
Hypocalcemic Disorders
1031(4)
Pseudohypoparathyroidism (Resistance to Parathyroid Hormone Action)
1035(1)
Hypercalcemic States
1035(2)
Familial Hypocalciuric Hypercalcemia (Familial Benign Hypercalcemia)
1037(1)
Hypervitaminosis D
1037(1)
Idiopathic Hypercalcemia of Infancy (Williams Syndrome)
1037(1)
Immobilization Hypercalcemia
1037(1)
Hypophosphatasia
1037(1)
Gonads (Ovaries & Testes)
1037(3)
Development
1037(1)
Disorders of Sexual Development
1038(2)
Abnormalities in Female Pubertal Development & Ovarian Function
1040(3)
Abnormalities in Male Pubertal Development & Testicular Function
1043(2)
Adrenal Cortex
1045(9)
Adrenocortical Insufficiency (Adrenal Crisis, Addison Disease)
1046(2)
Congenital Adrenal Hyperplasias
1048(2)
Adrenocortical Hyperfunction (Cushing Disease, Cushing Syndrome)
1050(1)
Primary Hyperaldosteronism
1051(1)
Uses of Glucocorticoids & Adrenocorticotropic Hormone in Treatment of Nonendocrine Diseases
1051(2)
Adrenal Medulla Pheochromocytoma
1053(1)
35 Diabetes Mellitus 1054(11)
Brigitte I. Frohnert
H. Peter Chase
Marian Rewers
General Considerations
1054(1)
Pathogenesis
1055(1)
Prevention
1055(1)
Clinical Findings
1055(1)
Differential Diagnosis
1056(1)
Complications
1056(3)
Associated Autoimmune Diseases in Type 1 Diabetes
1059(1)
Associated Conditions with Type 2 Diabetes
1060(1)
Treatment
1060(4)
Quality Assessment (QA) & Outcomes Metrics
1064(1)
Prognosis
1064(1)
References
1064(1)
36 Inborn Errors of Metabolism 1065(28)
Janet A. Thomas
Johan L.K. Van Hove
Peter R. Baker II
Introduction
1065(1)
Diagnosis
1065(2)
Suspecting Inborn Errors
1065(1)
Laboratory Studies
1066(1)
Common Clinical Situations
1066(1)
Management of Metabolic Emergencies
1067(1)
Newborn Screening
1067(1)
Disorders of Carbohydrate Metabolism
1068(3)
Glycogen Storage Diseases
1068(1)
Galactosemia
1069(1)
Hereditary Fructose Intolerance
1070(1)
Disorders of Energy Metabolism
1071(2)
Disorders of Amino Acid Metabolism
1073(6)
Disorders of the Urea Cycle
1073(1)
Phenylketonuria & the Hyperphenylalaninemias
1074(2)
Hereditary Tyrosinemia
1076(1)
Maple Syrup Urine Disease (Branched-Chain Ketoaciduria)
1077(1)
Homocystinuria
1077(1)
Nonketotic Hyperglycinemia
1078(1)
Organic Acidemias
1079(3)
Propionic & Methylmalonic Acidemia (Ketotic Hyperglycinemias)
1079(2)
Carboxylase Deficiency
1081(1)
Glutaric Acidemia Type I
1081(1)
Disorders of Fatty Acid Oxidation & Carnitine
1082(1)
Fatty Acid Oxidation Disorders
1082(1)
Carnitine
1083(1)
Purine Metabolism Disorders
1083(1)
Lysosomal Diseases
1084(3)
Peroxisomal Diseases
1087(1)
Congenital Disorders of Glycosylation
1088(1)
Smith-Lemli-Opitz Syndrome & Disorders of Cholesterol Synthesis
1089(1)
Disorders of Brain Specific Metabolism: Neurotransmitters, Synthesis of Amino Acids & Sphingolipids
1090(1)
Creatine Synthesis Disorders
1091(1)
Quality Initiatives in the Field of Metabolic Disease
1092(1)
37 Genetics & Dysmorphology 1093(31)
Naomi J.L. Meeks
Margarita Saenz
Anne Chun-Hui Tsai
Ellen R. Elias
Foundations of Genetic Diagnosis
1093(6)
Cytogenetics
1093(5)
Molecular Genetics
1098(1)
Principles of Inherited Human Disorders
1099(6)
Mendelian Inheritance
1099(3)
Multifactorial Inheritance
1102(1)
Nonmendelian Inheritance
1103(1)
Family History & Pedigree
1104(1)
Dysmorphology & Human Embryology
1105(2)
Mechanisms
1105(1)
Clinical Dysmorphology
1106(1)
Chromosomal Disorders: Abnormal Number
1107(2)
Trisomies
1107(1)
Sex Chromosome Abnormalities
1108(1)
Chromosomal Abnormalities: Abnormal Structure
1109(1)
Chromosome Deletion Disorders
1109(1)
Contiguous Gene Disorders
1109(1)
Mendelian Disorders
1110(5)
Autosomal Dominant Disorders
1110(3)
Autosomal Recessive Disorders
1113(1)
X-Linked Disorders
1114(1)
Nonmendelian Disorders
1115(1)
Disorders of Imprinting
1115(1)
Disorders Associated with Anticipation
1116(1)
Disorders of Multifactorial Inheritance
1116(3)
Cleft Lip & Cleft Palate
1117(1)
Neural Tube Defects
1118(1)
Common Recognizable Disorders with Variable or Unknown Cause
1119(1)
Genetic Evaluation of the Child with Developmental Disabilities
1120(2)
Perinatal Genetics
1122(2)
Teratogens
1122(1)
Assisted Reproduction
1122(1)
Prenatal Diagnosis
1123(1)
38 Allergic Disorders 1124(39)
Ronina A. Covar
David M. Fleischer
Christine Cho
Mark Boguniewicz
Introduction
1124(1)
Asthma
1124(19)
Allergic Rhinoconjunctivitis
1143(5)
Atopic Dermatitis
1148(4)
Urticaria & Angioedema
1152(2)
Anaphylaxis
1154(2)
Adverse Reactions to Drugs & Biologicals
1156(3)
Food Allergy
1159(2)
Insect Allergy
1161(2)
39 Antimicrobial Therapy 1163(24)
Sarah K. Parker
Jason Child
Justin Seams
John W. Ogle
Principles of Antimicrobial Therapy
1163(1)
Susceptibility Testing & Drug Dosing Properties
1163(1)
Pharmacodynamic Concepts
1164(1)
Use of Antimicrobial Agents to Prevent Disease
1165(1)
Concepts for Judicious Use of Antimicrobials
1165(2)
Choice of Antimicrobial Agents
1167(1)
Specific Antimicrobial Agents
1167(18)
β-Lactam Antibiotics (Step 1, Figure 39-2)
1167(8)
β-Lactam: Penicillin
1175(6)
β-Lactam: Cephems
1181(1)
β-Lactam: Monobactams
1181(1)
β-Lactam: Carbapenems
1181(1)
Glycopeptide Agents (Step 2, Figure 39-2)
1182(1)
Daptomycin (Step 4, Figure 39-2)
1182(1)
Trimethoprim/Sulfamethoxazole (Step 5, Figure 39-2)
1182(1)
Metronidazole (Step 6, Figure 39-2)
1183(1)
Macrolides (Step 6, Figure 39-2)
1183(1)
Lincosamides (Step 6, Figure 39-2)
1183(1)
Oxazolidinones (Step 6, Figure 39-2)
1184(1)
Tetracyclines (Step 6, Figure 39-2)
1184(1)
Aminoglycosides (Step 6, Figure 39-2)
1184(1)
Rifamycins (Step 7, Figure 39-2)
1185(1)
Fluoroquinolones (Step 8, Figure 39-2)
1185(1)
References
1185(2)
40 Infections: Viral & Rickettsial 1187(46)
Myron J. Levin
Daniel Olson
Edwin J. Asturias
Adriana Weinberg
Viral Infections
1187(11)
Respiratory Infections
1187(1)
Viruses Causing the Common Cold
1187(3)
Infections due to Adenoviruses
1190(4)
Influenza
1194(1)
Parainfluenza (Croup)
1195(1)
Respiratory Syncytial Virus Disease
1196(2)
Human Metapneumovirus Infection
1198(1)
Infections due to Enteroviruses & Parechoviruses
1198(5)
Acute Febrile Illness
1199(1)
Respiratory Tract Illnesses
1199(1)
Rashes (Including Hand-Foot-&- Mouth Disease)
1200(1)
Central Nervous System Illnesses
1200(3)
Infections due to Herpesviruses
1203(11)
Herpes Simplex Infections
1203(3)
Varicella & Herpes Zoster
1206(2)
Roseola Infantum (Exanthem Subitum)
1208(1)
Cytomegalovirus Infections
1209(3)
Infectious Mononucleosis (Epstein-Barr Virus)
1212(2)
Viral Infections Spread by Insect Vectors
1214(8)
Encephalitis
1214(4)
Dengue
1218(1)
Chikungunya
1219(1)
Zika
1220(1)
Colorado Tick Fever
1221(1)
Other Major Viral Childhood Exanthems
1222(4)
Erythema Infectiosum
1222(1)
Measles (Rubeola)
1223(2)
Rubella
1225(1)
Infections due to Other Viruses
1226(3)
Hantavirus Cardiopulmonary Syndrome
1226(1)
Mumps
1227(1)
Rabies
1228(1)
Rickettsial Infections & Q Fever
1229(6)
Human Ehrlichiosis & Anaplasmosis
1230(1)
Rocky Mountain Spotted Fever
1231(1)
Endemic Typhus (Murine Typhus)
1231(1)
Q Fever
1232(1)
41 Human Immunodeficiency Virus Infection 1233(13)
Elizabeth J. McFarland
Perinatally HIV-Exposed Infant
1235(1)
Adolescents with HIV Exposure
1236(1)
Progressive HIV Disease
1237(3)
Treatment
1240(4)
Prevention
1244(1)
Quality Assurance & Outcome Metrics
1245(1)
42 Infections: Bacterial & Spirochetal 1246(65)
James Gaensbauer
Yosuke Nomura
John W. Ogle
Marsha S. Anderson
Bacterial Infections
1246(56)
Group A Streptococcal Infections
1246(4)
Group B Streptococcal Infections
1250(3)
Streptococcal Infections with Organisms Other than Group A or B
1253(1)
Pneumococcal Infections
1254(3)
Staphylococcal Infections
1257(4)
Meningococcal Infections
1261(3)
Gonococcal Infections
1264(3)
Botulism
1267(2)
Tetanus
1269(1)
Gas Gangrene
1270(1)
Diphtheria
1271(2)
Infections due to Enterobacteriaceae
1273(2)
Pseudomonas Infections
1275(2)
Salmonella Gastroenteritis
1277(2)
Typhoid Fever & Paratyphoid Fever
1279(1)
Shigellosis (Bacillary Dysentery)
1280(1)
Cholera
1281(2)
Campylobacter Infection
1283(1)
Tularemia
1284(1)
Plague
1285(2)
Haemophilus Influenzae Type B Infections
1287(2)
Pertussis (Whooping Cough)
1289(2)
Listeriosis
1291(2)
Tuberculosis
1293(3)
Infections with Nontuberculous Mycobacteria
1296(2)
Legionella Infection
1298(1)
Chlamydophila er Chlamydia Infections (Psittacosis, C Pneumoniae, & C Trachomatis)
1299(2)
Cat-Scratch Disease
1301(1)
Spirochetal Infections
1302(9)
Syphilis
1302(3)
Relapsing Fever
1305(1)
Leptospirosis
1306(2)
Lyme Disease
1308(3)
43 Infections: Parasitic & Mycotic 1311(40)
James Gaensbauer
Kevin Messacar
Samuel R. Dominguez
Myron J. Levin
Parasitic Infections
1311(1)
Protozoal Infections
1312(13)
Systemic Infections
1312(7)
Gastrointestinal Infections
1319(5)
Trichomoniasis
1324(1)
Metazoal Infections
1325(10)
Nematode Infections
1325(6)
Cestode Infections (Flukes)
1331(3)
Trematode Infections
1334(1)
Mycotic Infections
1335(16)
Pneumocystis & Other Opportunistic Fungal Infections
1346(2)
Pneumocystis Jiroveci Infection
1348(3)
44 Sexually Transmitted Infections 1351(22)
Daniel H. Reirden
Ann-Christine Nyquist
Adolescent Sexuality
1351(1)
Risk Factors
1352(1)
Prevention of Sexually Transmitted Infections
1352(1)
Screening for Sexually Transmitted Infections
1352(1)
Signs & Symptoms
1353(1)
The Most Common Antibiotic- Responsive Sexually Transmitted Infections
1353(7)
Chlamydia Trachomatis Infection
1353(1)
Neisseria Gonorrhoeae Infection
1354(6)
The Spectrum of Signs & Symptoms of Sexually Transmitted Infections
1360(12)
Cervicitis
1360(1)
Pelvic Inflammatory Disease
1361(1)
Urethritis
1362(1)
Epididymitis
1363(1)
Proctitis, Proctocolitis, & Enteritis
1363(1)
Vaginal Discharge
1364(1)
Genital Ulcerations
1365(3)
Genital Warts & Human Papillomavirus
1368(2)
Other Viral Infections
1370(1)
Ectoparasitic Infections
1371(1)
References
1372(1)
45 Travel Medicine 1373(16)
Suchitra Rao
Introduction
1373(1)
Preparing Children & Infants for Travel
1373(2)
Vaccinations-Routine Childhood Vaccines Modified for Travel
1375(2)
Vaccinations-Travel-Specific
1377(2)
Traveler's Diarrhea
1379(1)
Malaria Prophylaxis & Prevention
1380(1)
Visits to Friends & Relatives (VFR) in High-Risk Areas
1381(1)
HIV & Sexually Transmitted Diseases
1381(3)
Fever in the Returned Traveler
1384(4)
References
1388(1)
46 Chemistry & Hematology Reference Intervals 1389(16)
Jordana E. Hoppe
Robert Snyder
Frank J. Accurso
Georgette Siparsky
Challenges in Determining & Interpreting Pediatric Reference Intervals
1389(1)
Guidelines for Use of Data in a Reference Range Study
1389(1)
Statistical Computation of Reference Intervals
1390(1)
Why Reference Intervals Vary
1391(1)
Sensitivity & Specificity
1391(1)
Pediatric Reference Intervals
1392(13)
Index 1405
William W. Hay, Jr., MD Professor, Department of Pediatrics Director, Training Program in Neonatal-Perinatal Medicine Director, Neonatal Clinical Research Center University of Colorado School of Medicine and The Childrens Hospital, Denver





Myron J. Levin, MD Professor, Departments of Pediatrics and Medicine Head, Section of Pediatric Infectious Diseases University of Colorado School of Medicine and The Childrens Hospital, Denver





Robin R. Deterding, MD Associate Professor of Pediatrics; Director, Division of Pediatric Pulmonology